Archives of Plastic Surgery

Korean Society of Plastic and Reconstructive Surgeons (대한성형외과학회)
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Bilateral Digital Extensor Hypoplasia Correction: A Case Report and Systematic Review

  • Marudeen Aivaz (Division of Plastic and Reconstructive Surgery, Children's National Hospital) ;
  • Esperanza Mantilla-Rivas (Division of Plastic and Reconstructive Surgery, Children's National Hospital) ;
  • Ashleigh Brennan (Division of Plastic and Reconstructive Surgery, Children's National Hospital) ;
  • John Thomas (Division of Plastic and Reconstructive Surgery, Children's National Hospital) ;
  • Elizabeth L. Malphrus (Division of Plastic and Reconstructive Surgery, Children's National Hospital) ;
  • Monica Manrique (Division of Plastic and Reconstructive Surgery, Children's National Hospital) ;
  • Albert K. Oh (Division of Plastic and Reconstructive Surgery, Children's National Hospital) ;
  • Gary F. Rogers (Division of Plastic and Reconstructive Surgery, Children's National Hospital)
  • Received : 2022.01.21
  • Accepted : 2022.08.11
  • Published : 2023.03.15
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Abstract

Digital extensor hypoplasia (DEH) is a rare malformation that presents with loss of active finger extension at the metacarpophalangeal (MCP) joints. Descriptions of optimal treatment and outcomes in this population are sparse. We describe successful operative treatment of a child with DEH involving the extensor digitorum communis, extensor digiti minimi, and the extensor indicis proprius tendons. The 5-year-old male patient was referred for severe limitation on bilateral finger extension since birth. He had been previously diagnosed with arthrogryposis and managed conservatively. Due to lack of improvement, magnetic resonance imaging was done evidencing hypoplasia/aplasia of the extensor tendons. The patient underwent successful tendon transfers using extensor carpi radialis longus to the common extensor tendons, and one hand required an additional tenolysis procedure. 2 years postoperatively, his MCP position and finger extension are markedly improved, and he is able to grip objects without limitation or difficulty. The patient returned to full activity without restriction.

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References

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