Journal of the Korean Society of Radiology (대한영상의학회지)

The Korean Society of Radiology (대한영상의학회)
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Primary Malignant Peripheral Nerve Sheath Tumor of the Pulmonary Vein: A Case Report

폐정맥의 원발성 악성 말초신경초종: 증례 보고

  • Hyun Woo (Department of Radiology, Chungnam National University Hospital, Chungnam National University School of Medicine) ;
  • Hyeyoung Kwon (Department of Radiology, Chungnam National University Hospital, Chungnam National University School of Medicine) ;
  • Jin Hwan Kim (Department of Radiology, Chungnam National University Hospital, Chungnam National University School of Medicine) ;
  • Song Soo Kim (Department of Radiology, Chungnam National University Hospital, Chungnam National University School of Medicine) ;
  • Hyung Kyu Park (Department of Pathology, Chungnam National University Hospital, Chungnam National University School of Medicine) ;
  • Younju Rhee (Department of Thoracic and Cardiovascular Surgery, Chungnam National University Hospital, Chungnam National University School of Medicine) ;
  • Jae-Hyeong Park (Department of Cardiology in Internal Medicine, Chungnam National University Hospital, Chungnam National University School of Medicine)
  • 우현 (충남대학교 의과대학 충남대학교병원 영상의학과) ;
  • 권혜영 (충남대학교 의과대학 충남대학교병원 영상의학과) ;
  • 김진환 (충남대학교 의과대학 충남대학교병원 영상의학과) ;
  • 김성수 (충남대학교 의과대학 충남대학교병원 영상의학과) ;
  • 박형규 (충남대학교 의과대학 충남대학교병원 병리과) ;
  • 이연주 (충남대학교 의과대학 충남대학교병원 흉부외과) ;
  • 박재형 (충남대학교 의과대학 충남대학교병원 심장내과)
  • Received : 2023.01.03
  • Accepted : 2023.07.08
  • Published : 2023.11.01
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Abstract

Primary masses rarely originate from the heart and great vessels, and a malignant peripheral nerve sheath tumor (MPNST) is extremely rare. A 76-year-old male with pleural effusion underwent contrast-enhanced computed tomography, which revealed a hypoattenuating mass involving the right pulmonary vein and left atrium. Ultrasonography showed that the mass originated from the right pulmonary vein. Surgical resection confirmed an MPNST that originated from the pulmonary vein. We report the first Korean case of a primary MPNST originating from the pulmonary vein. We have also described the radiologic findings suggestive of a pulmonary vein mass.

심장과 대혈관 기원의 원발성 종괴는 매우 드물다. 그중에서도 악성 말초신경초종은 더 드물게 보고되었다. 76세 남성에서 발견된 흉수의 원인 평가를 위해 시행한 조영증강 컴퓨터단층촬영에서 우폐정맥과 좌심방을 침범하는 저음영의 종괴가 발견되었고 초음파상 우폐정맥에서 기인한 종괴로 의심되었다. 종괴는 수술적 절제를 통해 폐정맥 기원의 악성 말초신경초종으로 최종 진단되었다. 저자들은 국내에서 보고된 바가 없는 드문 증례인 폐정맥 기원의 원발성 악성 말초신경초종을 보고하고, 종괴가 폐정맥 기원임을 시사하는 영상의학적 소견에 대해 고찰하고자 한다.

Keywords

References

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