Journal of the Korean Society of Radiology (대한영상의학회지)

The Korean Society of Radiology (대한영상의학회)
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Pulmonary Artery Intimal Sarcoma Involving the Peripheral Pulmonary Artery, Initially Misdiagnosed as Pulmonary Artery Thromboembolism and Vasculitis: A Case Report

폐동맥 혈전색전증과 혈관염으로 오진된 주변부 폐동맥에서 발생한 폐동맥 내막육종: 증례 보고

  • Min Seong Kim (Department of Radiology, Keimyung University School of Medicine, Dongsan Medical Center) ;
  • Jin Hee Lee (Department of Radiology, Keimyung University School of Medicine, Dongsan Medical Center) ;
  • Jung Hee Hong (Department of Radiology, Keimyung University School of Medicine, Dongsan Medical Center) ;
  • Il Seon Hwang (Department of Pathology, Keimyung University School of Medicine, Dongsan Medical Center)
  • 김민성 (계명대학교 의과대학 동산병원 영상의학과) ;
  • 이진희 (계명대학교 의과대학 동산병원 영상의학과) ;
  • 홍정희 (계명대학교 의과대학 동산병원 영상의학과) ;
  • 황일선 (계명대학교 의과대학 동산병원 병리과)
  • Received : 2022.12.26
  • Accepted : 2023.06.11
  • Published : 2023.11.01
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Abstract

Pulmonary artery sarcomas are rare, high-grade malignancies, primarily affecting the proximal elastic pulmonary artery and usually manifesting as tumoral impaction on imaging. Due to similar clinical and imaging findings, pulmonary artery sarcomas are frequently misdiagnosed as pulmonary thromboembolism or, occasionally, as vasculitis. Herein, we reported a case of pulmonary artery intimal sarcoma initially misdiagnosed as pulmonary thromboembolism and vasculitis due to its relatively atypical location and morphology, along with a literature review.

폐동맥 육종은 매우 드문 고등급 악성종양으로, 주로 근위부의 탄력형 폐동맥에, 대개는 종양 충만(tumoral impaction)의 형태로 나타난다. 임상양상과 영상학적 소견이 유사하여 주로 폐 혈전색전증으로 오인되며 가끔 혈관염으로 오인되기도 한다. 우리는 비교적 드문 위치와 형태로 인해 폐 혈전색전증과 혈관염으로 오인했던 폐동맥 내막육종을 경험하였기에 문헌고찰과 더불어 증례를 보고하고자 한다.

Keywords

References

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