대한영상의학회지 (Journal of the Korean Society of Radiology)

  • 제84권2호
  • /
  • Pages.472-476
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  • 2023
  • /
  • 1738-2637(pISSN)
  • /
  • 2288-2928(eISSN)
대한영상의학회 (The Korean Society of Radiology)
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코뼈에 발생한 랑게르한스 세포 조직구증: 증례 보고

Langerhans Cell Histiocytosis in the Nasal Bone: A Rare Case

  • 안원익 (대구파티마병원 영상의학과) ;
  • 장종창 (대구파티마병원 영상의학과) ;
  • 양동진 (대구파티마병원 영상의학과) ;
  • 김태은 (대구파티마병원 영상의학과) ;
  • 박효천 (대구파티마병원 성형외과) ;
  • 이동규 (대구파티마병원 성형외과) ;
  • 성재민 (대구파티마병원 성형외과)
  • Won Ik Ahn (Department of Radiology, Daegu Fatima Hospital) ;
  • Jong Chang Jang (Department of Radiology, Daegu Fatima Hospital) ;
  • Dong Jin Yang (Department of Radiology, Daegu Fatima Hospital) ;
  • Tae Eun Kim (Department of Radiology, Daegu Fatima Hospital) ;
  • Hyou Chun Park (Department of Plastic and Reconstructive Surgery, Daegu Fatima Hospital) ;
  • Dong Kyu Lee (Department of Plastic and Reconstructive Surgery, Daegu Fatima Hospital) ;
  • Jae Min Seong (Department of Plastic and Reconstructive Surgery, Daegu Fatima Hospital)
  • 투고 : 2022.01.10
  • 심사 : 2022.07.20
  • 발행 : 2023.03.01
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초록

코뼈에 발생하는 랑게르한스 세포 조직구증 증례는 거의 보고된 적이 없다. 저자들은 왼쪽 코에 만져지는 종괴를 주소로 내원한 13세 환자를 검사하였다. 초음파 검사상 코 좌측에 저음영 에코를 보이는 종괴가 관찰되었다. 자기공명영상 검사에서 경계가 분명하면서 비교적 균질한 조영증강을 보이는 종괴가 관찰되었다. 조직병리학적 검사에서 검체는 랑게르한스 세포 조직구증으로 확인되었다.

Nasal bone involvement of Langerhans cell histiocytosis is rarely reported. Here we present a case of a 13-year-old boy with a palpable nasal mass. Ultrasonography revealed a hypoechoic mass on the left side of the nose. Both CT scanning and MRI showed an osteolytic mass. The lesion seen on MRI was well-defined mass with homogeneous enhancement. Histopathological examination of the resected specimen confirmed the diagnosis of LCH.

키워드

참고문헌

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