대한영상의학회지 (Journal of the Korean Society of Radiology)

  • 제83권2호
  • /
  • Pages.372-377
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  • 2022
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  • 1738-2637(pISSN)
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  • 2951-0805(eISSN)
대한영상의학회 (The Korean Society of Radiology)
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고령에서 일측성 간질성 폐질환으로 보이는 일측성 폐정맥 폐쇄: 흉부 X선 사진의 시계열적 변화와 문헌 고찰

Unilateral Pulmonary Vein Atresia Initially Presenting as Interstitial Lung Disease in an Elderly Female: Serial Chest Radiograph Changes and Its Literature Review

  • 심영우 (영남대학교 의과대학 영남대학교병원 영상의학과) ;
  • 박종민 (경북대학교 의과대학 영상의학교실) ;
  • 박병건 (경북대학교 의과대학 영상의학교실) ;
  • 임재광 (경북대학교 의과대학 영상의학교실) ;
  • 신경민 (경북대학교 의과대학 영상의학교실) ;
  • 김영선 (영남대학교 의과대학 영남대학교병원 영상의학과)
  • Young Woo Sim (Department of Radiology, Yeungnam University Hospital, Yeungnam University College of Medicine) ;
  • Jongmin Park (Department of Radiology, School of Medicine, Kyungpook National University) ;
  • Byunggeon Park (Department of Radiology, School of Medicine, Kyungpook National University) ;
  • Jae-Kwang Lim (Department of Radiology, School of Medicine, Kyungpook National University) ;
  • Kyung Min Shin (Department of Radiology, School of Medicine, Kyungpook National University) ;
  • Young-Seon Kim (Department of Radiology, Yeungnam University Hospital, Yeungnam University College of Medicine)
  • 투고 : 2021.02.18
  • 심사 : 2021.05.30
  • 발행 : 2022.03.01
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초록

일측성 폐정맥 폐쇄는 총폐정맥이 좌심방내로 연결되는 못하는 드문 심혈관계 기형이다. 일측성 폐정맥 폐쇄는 흔히 어린 시기에 진단이 되며, 성인이 된 이후에 진단이 되는 경우는 극히 드물다. 성인 환자에서 활동 시 호흡곤란과 객혈이 흔한 임상증상이다. 폐실질의 이상은 폐정맥 폐쇄의 간접적인 소견이며, 간질성 폐질환으로 나타날 수 있다. 우리는 62세 여자 환자에서 일측성 간질성 폐질환을 보이는 일측성 폐정맥 폐쇄의 증례와 12년간의 흉부 X선 사진 소견의 변화를 보고하고자 한다.

Unilateral pulmonary vein atresia (PVA) is a rare congenital cardiovascular anomaly occurring after the common pulmonary vein fails to incorporate into the left atrium. It is most commonly diagnosed in childhood, and diagnosis after reaching adulthood is extremely rare. Dyspnea on exertion and hemoptysis are common clinical features in adult PVA patients, whereas lung parenchymal abnormalities are indirect signs of PVA, which can manifest as interstitial lung disease. Herein, we present the case of a 62-year-old female diagnosed with unilateral PVA presenting as unilateral interstitial lung disease and report the changes in her chest radiographs over 12 years.

키워드

참고문헌

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