Journal of the Korean Society of Radiology (대한영상의학회지)

The Korean Society of Radiology (대한영상의학회)
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Carotid Vessel Wall MRI Findings in Acute Cerebral Infarction Caused by Polycythemia Vera: A Case Report

적혈구 증가증으로 인한 급성 뇌경색에서 경동맥 혈관벽 자기공명영상 소견: 증례 보고

  • Jun Kyeong Park (Department of Radiology, Dongguk University Ilsan Hospital) ;
  • Eun Ja Lee (Department of Radiology, Dongguk University Ilsan Hospital) ;
  • Dong-Eog Kim (Department of Neurology, Dongguk University Ilsan Hospital) ;
  • Hyun Jung Lee (Division of Hematology and Medical Oncology, Department of Internal Medicine, Dongguk University Ilsan Hospital)
  • 박준경 (동국대학교 의과대학 영상의학과) ;
  • 이은자 (동국대학교 의과대학 영상의학과) ;
  • 김동억 (동국대학교 의과대학 신경과) ;
  • 이현정 (동국대학교 의과대학 혈액종양내과)
  • Received : 2021.06.03
  • Accepted : 2021.08.23
  • Published : 2022.01.01
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Abstract

Polycythemia vera (PV) is a rare myeloproliferative disease that causes elevated absolute red blood cell (RBC) mass due to uncontrolled RBC production. Moreover, this condition has been associated with a high risk of ischemic stroke and large vessel stenosis or occlusion, with many studies reporting cerebral infarction in PV patients. Despite these findings, there have been no reports on the vessel wall MRI (VW-MRI) findings of the narrowed vessels in PV-associated ischemic stroke patients. To the best of our knowledge, this is the first report in English regarding the carotid VW-MRI findings of a 30-year-old male diagnosed with PV after being hospitalized due to stroke.

진성적혈구증가증은 드문 골수 증식성 질환이며 제어되지 않은 적혈구 생산으로 인해 절대 적혈구 질량이 증가한다. 진성적혈구증가증은 큰 혈관의 협착 또는 폐색과 함께 허혈성 뇌졸중의 위험이 높다. 진성적혈구증가증 환자에서 뇌경색에 대한 많은 증례 보고가 있다. 그러나 합병증으로 뇌졸중이 발생한 진성적혈구증가증 환자의 좁아진 혈관에서 혈관벽 자기공명영상 소견은 보고되지 않았다. 저자들은 뇌졸중으로 인해 입원한 후 PV로 진단된 30세 남성의 경동맥 VW-MRI 소견에 관해 보고하고자 하며, 이는 우리가 아는 한 영어로 된 첫 번째 보고이다.

Keywords

References

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