Archives of Craniofacial Surgery (대한두개안면성형외과학회지)

Korean Cleft Palate-Craniofacial Association (대한두개안면성형외과학회)
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Treatment of Morbihan disease

  • Kim, Joo Hyoung (Department of Plastic and Reconstructive Surgery, Pusan National University School of Medicine and Biomedical Research Institute, Pusan National University Hospital)
  • Received : 2021.05.10
  • Accepted : 2021.05.18
  • Published : 2021.06.20
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Abstract

Morbihan disease (MD) is a rare condition that involves rosaceous lymphedema or erythematous lymphedema of the middle and upper thirds of the face. It typically affects the periorbital region, forehead, glabella, nose, and cheeks. The etiology of MD remains unclear, and its diagnosis is challenging. MD often tends to be unresponsive to therapies commonly used to treat rosacea, including corticosteroids, isotretinoin, and antibiotics. Surgical treatments have therefore been attempted, but most cases showed unsatisfactory responses. These problems could have resulted from an incorrect recognition and interpretation of the pathophysiology of MD and inaccurate planning of the operation, resulting in recurrence or exacerbation of edema.

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Acknowledgement

This work was supported by clinical research grant from Pusan National University Hospital in 2021.

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