Korean Journal of Head & Neck Oncology (대한두경부종양학회지)

The Korean Society for Head and Neck Oncology (대한두경부종양학회)
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A Case of Hemophagocytic Lymphohistiocytosis Presenting with Neck Mass in a Child

경부 종괴를 동반한 소아에서의 혈구탐식성 림프조직구증 1례

  • Kil, Bu Kwan (Department of Otorhinolaryngology-Head and Neck Surgery, School of Medicine, Catholic University of Daegu) ;
  • Lee, Dong Won (Department of Otorhinolaryngology-Head and Neck Surgery, School of Medicine, Catholic University of Daegu) ;
  • Kim, Jeong Kyu (Department of Otorhinolaryngology-Head and Neck Surgery, School of Medicine, Catholic University of Daegu)
  • 길부관 (대구가톨릭대학교 의과대학 이비인후과학교실) ;
  • 이동원 (대구가톨릭대학교 의과대학 이비인후과학교실) ;
  • 김정규 (대구가톨릭대학교 의과대학 이비인후과학교실)
  • Received : 2020.07.08
  • Accepted : 2020.11.01
  • Published : 2020.11.30
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Abstract

Hemophagocytic lymphohistiocytosis (HLH) is a rare but life-threatening one syndrome of excessive immune activation. This immune dysregulation disorder is prominently associated with cytopenias and combinations of clinical signs and extreme inflammation symptoms. For survival, it is important to diagnose early and treat appropriately. We report a case of 10 years old boy who was admitted to the hospital with a month history of fever and cervical lymph node enlargement. There were signs of hemophagocytic histiocytosis in the lymph node and bone marrow. The etiology, diagnosis, and treatment of hemophagocytic lymphohistiocytosis are reviewed.

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References

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