Korean Journal of Head & Neck Oncology (대한두경부종양학회지)

The Korean Society for Head and Neck Oncology (대한두경부종양학회)
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IgG4 Related Disease Misdiagnosed to Carotid Body Tumor

경동맥소체종양으로 오인된 IgG4 연관 질환

  • Lee, Gun Hyuk (Department of Otorhinolaryngology-Head & Neck Surgery, College of Medicine, Catholic Kwandong University) ;
  • Song, Ji-Sun (Department of Pathology, College of Medicine, Catholic Kwandong University) ;
  • Yoon, So Yeon (Department of Otorhinolaryngology-Head & Neck Surgery, College of Medicine, Catholic Kwandong University) ;
  • Cho, Youn Jin (Department of Otorhinolaryngology-Head & Neck Surgery, College of Medicine, Catholic Kwandong University) ;
  • Hong, Hyun Jun (Department of Otorhinolaryngology-Head & Neck Surgery, College of Medicine, Catholic Kwandong University)
  • 이건혁 (가톨릭관동대학교 의과대학 이비인후-두경부외과학교실) ;
  • 송지선 (가톨릭관동대학교 의과대학 병리학교실) ;
  • 윤소연 (가톨릭관동대학교 의과대학 이비인후-두경부외과학교실) ;
  • 조윤진 (가톨릭관동대학교 의과대학 이비인후-두경부외과학교실) ;
  • 홍현준 (가톨릭관동대학교 의과대학 이비인후-두경부외과학교실)
  • Received : 2020.04.21
  • Accepted : 2020.07.21
  • Published : 2020.11.30
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Abstract

Neck mass has various etiologies, including inflammatory, congenital, neoplastic causes. The IgG4-related disease can cause symptoms in the head and neck areas with an inflammatory neck mass. It also shows clinical and pathological findings from inflammation caused by immune reactions, such as lymphocyte and plasma cell infiltration, storiform fibrosis, obliteration phlebitis, and invigorated serum IgG4 levels. The treatment guideline has not been established and still under debate, but systemic glucocorticoid seems to be effective in the most cases. In this brief report, a 48-year-old male patient presented with voice change for 3 weeks. Left side paramedian vocal fold palsy was observed in the flexible laryngoscopy. About 2.5×2.0×1.2cm size, heterogeneously enhanced neck mass with irregular margin encasing left carotid artery was noted on preoperative contrast enhanced neck CT scan, and it was suspicious of left carotid body tumor. The pathology shows IgG4-related disease rather than carotid body tumors. We report this case of IgG4-related disease, which can be misdiagnosed to carotid body tumors.

Keywords

References

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