Journal of the Korean Society of Radiology (대한영상의학회지)

The Korean Society of Radiology (대한영상의학회)
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Three-Dimensional Printed Model of Partial Anomalous Pulmonary Venous Return with Biatrial Connection

양측 심방 연결을 형성하는 부분 폐정맥 환류 이상의 3D 프린팅 모델

  • Myoung Kyoung Kim (Department of Radiology, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Sung Mok Kim (Department of Radiology, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Eun Kyoung Kim (Imaging Center, Heart Vascular Stroke Institute, Samsung Medical Center) ;
  • Sung-A Chang (Imaging Center, Heart Vascular Stroke Institute, Samsung Medical Center) ;
  • Tae-Gook Jun (Department of Thoracic and Cardiovascular Surgery, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Yeon Hyeon Choe (Department of Radiology, Samsung Medical Center, Sungkyunkwan University School of Medicine)
  • 김명경 (성균관대학교 의과대학 삼성서울병원 영상의학과) ;
  • 김성목 (성균관대학교 의과대학 삼성서울병원 영상의학과) ;
  • 김은경 (삼성서울병원 심뇌혈관병원 이미징센터) ;
  • 장성아 (삼성서울병원 심뇌혈관병원 이미징센터) ;
  • 전태국 (성균관대학교 의과대학 삼성서울병원 흉부외과) ;
  • 최연현 (성균관대학교 의과대학 삼성서울병원 영상의학과)
  • Received : 2020.02.06
  • Accepted : 2020.06.16
  • Published : 2020.11.01
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Abstract

Partial anomalous pulmonary venous return (PAPVR) is a rare congenital cardiac anomaly that can be difficult to detect and often remains undiagnosed. PAPVR is diagnosed using non-invasive imaging techniques such as echocardiography, CT, and MRI. Image data are reviewed on a 2-dimensional (D) monitor, which may not facilitate a good understanding of the complex 3D heart structure. In recent years, 3D printing technology, which allows the creation of physical cardiac models using source image datasets obtained from cardiac CT or MRI, has been increasingly used in the medical field. We report a case involving a 3D-printed model of PAPVR with a biatrial connection. This model demonstrated separate drainages of the right upper and middle pulmonary veins into the lower superior vena cava (SVC) and the junction between the SVC and the right atrium, respectively, with biatrial communication through the right middle pulmonary vein.

부분 폐정맥 환류 이상은 드문 선천성 폐정맥 기형의 한 종류로 진단 시 종종 간과될 수 있다. 대부분의 경우 비 침습적인 영상검사인 심장 초음파, CT 또는 MRI로 진단을 하게 되는데, 2D 모니터를 이용한 영상진단은 삼차원적으로 복잡한 심장의 구조를 이해하는데 제한이 있다. 최근에는 CT와 MRI에서 얻은 의료 영상 데이터를 기반으로 3D 프린팅 기술을 이용하여 심장의 모형을 만드는 기술이 소개되어 점차 이용이 증가되고 있다. 본 증례 보고에서 저자들은 우측 상 폐정맥과 우측 중 폐정맥이 상대정맥으로의 각각 배출되며 우측 중 폐정맥을 통해 양측 심방 간의 연결이 이루어진 환자의 CT 영상 및 3D 프린팅 모델에 대해 보고하고자 한다.

Keywords

Acknowledgement

This study was supported by the DongKook Life Science. Co., Ltd., Republic of Korea. Grant was used to pay for the creation of 3D printed model.

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