Journal of Dental Anesthesia and Pain Medicine

The Korean Dental Society of Anesthsiology (대한치과마취과학회)
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Concealed congenital long QT syndrome during velopharyngeal dysfunction correction: a case report

  • Jeon, Soeun (Department of Anesthesia and Pain Medicine, School of Medicine, Pusan National University) ;
  • Lee, Hyeon-Jeong (Department of Anesthesia and Pain Medicine, School of Medicine, Pusan National University) ;
  • Jung, Young-hoon (Department of Anesthesia and Pain Medicine, School of Medicine, Pusan National University) ;
  • Do, Wangseok (Department of Anesthesia and Pain Medicine, School of Medicine, Pusan National University) ;
  • Cho, Ah-Reum (Department of Anesthesia and Pain Medicine, School of Medicine, Pusan National University) ;
  • Baik, Jiseok (Department of Anesthesia and Pain Medicine, School of Medicine, Pusan National University) ;
  • Lee, Do-Won (Department of Anesthesia and Pain Medicine, School of Medicine, Pusan National University) ;
  • Kim, Eun-Jung (Department of Dental Anesthesia and Pain Medicine, School of Dentistry, Pusan National University, Dental Research Institute) ;
  • Kim, Eunsoo (Department of Anesthesia and Pain Medicine, School of Medicine, Pusan National University) ;
  • Hong, Jeong-Min (Department of Anesthesia and Pain Medicine, School of Medicine, Pusan National University)
  • Received : 2020.04.08
  • Accepted : 2020.05.12
  • Published : 2020.06.30
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Abstract

The congenital long QT syndrome (LQTS) is an inherited cardiac disorder characterized by increased QT intervals and a tendency to experience ventricular tachycardia, which can cause fainting, heart failure, or sudden death. A 4-year-old female patient undergoing velopharyngeal correction surgery under general anesthesia suddenly developed Torsades de pointes. Although the patient spontaneously resolved to sinus rhythm without treatment, subsequent QT prolongation persisted. Here, we report a case of concealed LQTS with a literature review.

Keywords

References

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