Archives of Plastic Surgery

Korean Society of Plastic and Reconstructive Surgeons (대한성형외과학회)
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Anorectal malformation with didelphys uterus: Extremely rare anomaly and successful neoanal sphincter reconstruction with gracilis muscle flap

  • Burusapat, Chairat (Division of Plastic and Reconstructive Surgery, Department of Surgery, Phramongkutklao Hospital) ;
  • Hongkarnjanakul, Natthawoot (Division of Plastic and Reconstructive Surgery, Department of Surgery, Phramongkutklao Hospital) ;
  • Wanichjaroen, Nutthapong (Division of Plastic and Reconstructive Surgery, Department of Surgery, Phramongkutklao Hospital) ;
  • Panitwong, Sakchai (Division of Reproductive Medicine, Department of Obstetrics and Gynecology, Phramongkutklao Hospital, Phramongkutklao College of Medicine) ;
  • Sangkaewsuntisuk, Jiraporn (Division of Colorectal Surgery, Department of Surgery, Phramongkutklao Hospital, Phramongkutklao College of Medicine) ;
  • Boonya-ussadorn, Chinakrit (Division of Colorectal Surgery, Department of Surgery, Phramongkutklao Hospital, Phramongkutklao College of Medicine)
  • Received : 2019.08.01
  • Accepted : 2019.11.30
  • Published : 2020.05.15
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Abstract

Anorectal malformation or imperforate anus is a congenital anomaly of rectum and anus. Mullerian duct anomalies are abnormal development of uterus, cervix, and vagina. Imperforate anus with double uterus is extremely rare and cannot explain by normal embryologic development. Moreover, guideline in treatment is inconclusive. We report an extremely rare case of a young adult female who presented with recurrent pelvic inflammatory disease caused by rectovaginal fistula in congenital imperforate anus and didelphys uterus, and successfully neoanal reconstruction with gracilis muscle flap. Aims for treatment are closed rectovaginal fistula, and anal sphincter reconstruction. To our best knowledge, the imperforate anus with double uterus is extremely rare anomaly. Furthermore, successfully anal sphincter reconstruction with functional gracilis muscle in the imperforate anus with double uterus has never been reported in English literature.

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References

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