Annals of Clinical Neurophysiology

The Korean Society of Clinical Neurophysiology (대한임상신경생리학회)
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Motor dominant polyradiculopathy with Primary Sjögren's syndrome mimicking motor neuron disease

  • Ahn, Suk-Won (Department of Neurology, Chung-Ang University Hospital, Chung-Ang University College of Medicine) ;
  • Yoon, Byung-Nam (Department of Neurology, Seoul Paik Hospital, Inje University College of Medicine)
  • Received : 2018.09.19
  • Accepted : 2018.12.25
  • Published : 2019.01.31
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Abstract

$Sj{\ddot{o}}gren^{\prime}s$ syndrome (SS)-associated polyradiculopathy is rarely reported. A 51-year-old woman presented with a history of gradual weakness in all four extremities for several months. Based on electrophysiological studies, spinal magnetic resonance imaging and cerebrospinal fluid examination, inflammatory polyradiculopathy was confirmed. During a search for the aetiology, the patient was ultimately diagnosed with SS. This study introduces SS-associated polyradiculopathy that primarily presented with motor symptoms, thus mimicking motor neuron disease.

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References

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