Journal of Electrodiagnosis and Neuromuscular Diseases (대한근전도전기진단의학회지)

Korean Association of EMG Electrodiagnostic Medicine (대한근전도전기진단의학회)
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Bibrachial Amyotrophy Associated with Epidural Cerebrospinal Fluid Leakage: A Case Report

경막외 뇌척수액 누출과 연관된 양측 상지 근위축증: 증례보고

  • Rho, Hyunwoo (Department of Physical and Rehabilitation Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Jeong, Jiseon (Department of Physical and Rehabilitation Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Sung, Duk Hyun (Department of Physical and Rehabilitation Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine)
  • 노현우 (성균관대학교 의과대학 삼성서울병원 재활의학과) ;
  • 정지선 (성균관대학교 의과대학 삼성서울병원 재활의학과) ;
  • 성덕현 (성균관대학교 의과대학 삼성서울병원 재활의학과)
  • Received : 2018.03.16
  • Accepted : 2018.06.27
  • Published : 2018.12.31
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Abstract

We describe a case of a 71-year-old male patient who experienced progressive bilateral proximal upper limb weakness and atrophy without sensory symptoms and signs over 5 years. Electromyography demonstrated denervation potentials and neuropathic motor unit action potentials on C5-C7 myotome muscles bilaterally. Cervical spine magnetic resonance imaging revealed engorged anterior epidural venous plexus, T2 hyperintensity localized to grey matter ("snake-eye" appearance) at C2-C6 vertebral level, and ventral epidural fluid collection from C6 to T8 vertebral level. This case indicates that bibrachial amyotrophy associated with epidural fluid leak should be suspected in patients presenting with progressive bilateral upper limb weakness and atrophy without sensory involvement.

Keywords

References

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