Kosin Medical Journal (고신대학교 의과대학 학술지)

Kosin University College of Medicine (고신대학교 의과대학)
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A Case of Long-term Survival in a Patient with Primary Primitive Neuroectodermal Tumor of the Lung

  • Kang, Lae Hyung (Department of Internal Medicine Pusan National University Yangsan Hospital, Pusan National University School of Medicine) ;
  • Kim, Hyeong Jin (Department of Internal Medicine Pusan National University Yangsan Hospital, Pusan National University School of Medicine) ;
  • Jang, Jin Ho (Department of Internal Medicine Pusan National University Yangsan Hospital, Pusan National University School of Medicine) ;
  • Kim, Jun Hyun (Department of Internal Medicine Pusan National University Yangsan Hospital, Pusan National University School of Medicine) ;
  • Choi, Kyoung Un (Department of Pathology, Pusan National University Yangsan Hospital, Pusan National University School of Medicine) ;
  • Jeon, Doosoo (Department of Internal Medicine Pusan National University Yangsan Hospital, Pusan National University School of Medicine)
  • Received : 2016.06.06
  • Accepted : 2016.09.18
  • Published : 2018.12.31
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Abstract

Primitive neuroectodermal tumor (PNET) arising primarily in the lung is an extremely rare and aggressive malignancy with poor chances of patient survival. We present a case of long-term survival by a 29-year-old woman with PNET diagnosed after a hertological and immunohertochemical examination of a biopsy specimen obtained by performing video-assisted thoracic surgery. The patient underwent a left lower lung lobe lobectomy and 6 cycles of adjuvant chemotherapy. The patient has been free of any symptoms of the recurrence of the disease for 6 years after treatment completion.

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References

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