The Korean Journal of Medicine

  • 제93권5호
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  • Pages.492-496
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  • 2018
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  • 1738-9364(pISSN)
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  • 2289-0769(eISSN)
대한내과학회 (The Korean Association of Internal Medicine)
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강직척추염 발병 이후 전신경화증과 흉수가 동반된 1예

Systemic Sclerosis and Pleural Effusion in a Patient with Ankylosing Spondylitis

  • 구본산 (인제대학교 의과대학 서울백병원 내과) ;
  • 송윤아 (한양대학교 류마티스병원 영상의학과) ;
  • 이승훈 (한양대학교 류마티스병원 영상의학과) ;
  • 김태환 (한양대학교 류마티스병원 류마티스내과) ;
  • 전재범 (한양대학교 류마티스병원 류마티스내과)
  • Koo, Bon San (Department of Internal Medicine, Inje University Seoul Paik Hospital, Inje University College of Medicine) ;
  • Song, Yoonah (Department of Radiology, Hanyang University Hospital for Rheumatic Diseases) ;
  • Lee, Seunghun (Department of Radiology, Hanyang University Hospital for Rheumatic Diseases) ;
  • Kim, Tae-Hwan (Department of Rheumatology, Hanyang University Hospital for Rheumatic Diseases) ;
  • Jun, Jae-Bum (Department of Rheumatology, Hanyang University Hospital for Rheumatic Diseases)
  • 투고 : 2017.12.05
  • 심사 : 2018.03.01
  • 발행 : 2018.10.01
⟨ 이전 논문 다음 논문 ⟩

초록

Systemic sclerosis (SSc) is a chronic autoimmune disorder characterized by endothelial and fibroblast dysfunction, resulting in progressive fibrosis of the skin and internal organs. Ankylosing spondylitis (AS) is an arthritic condition affecting the axial skeleton and peripheral joints. An association between SSc and AS is relatively rare, as the two diseases share few characteristics. Here, we present a case of limited SSc in a 44-year-old man who exhibited low-grade AS, and discuss several cases of coexisting SSc and AS in the literature. Patients with both diseases showed several common features, including male predominance, middle age, and combined interstitial lung disease. However, unlike our case, the patients reported in the literature had advanced ankylosis and diffuse SSc.

키워드

참고문헌

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