임상이비인후과 (Journal of Clinical Otolaryngology Head and Neck Surgery)

  • 제29권2호
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  • Pages.240-244
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  • 2018
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  • 1225-0244(pISSN)
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  • 2713-833X(eISSN)
대한이비인후과학회 부산,울산,경남 지부회 (The Busan, Ulsan, Gyeoungnam Branch of Korean Society of Otolaryngology-Head and Neck Surgery)
권호 표지

안면 마비와 난청으로 진단된 면역글로불린 G4 연관질환 동반 육아종성 다발 혈관염 1예

A Case of Granulomatosis with Polyangiitis with IgG4-Related Disease Expressed by Facial Paralysis and Hearing Loss

  • 김형식 (경희대학교 의과대학.의학전문대학원 이비인후과학교실) ;
  • 두전강 (경희대학교 의과대학.의학전문대학원 이비인후과학교실) ;
  • 여승근 (경희대학교 의과대학.의학전문대학원 이비인후과학교실) ;
  • 김상훈 (경희대학교 의과대학.의학전문대학원 이비인후과학교실)
  • Kim, Hyung-sik (Department of Otorhinolaryngology-Head and Neck Surgery, School of Medicine, Kyung Hee University) ;
  • Doo, Jeon Gang (Department of Otorhinolaryngology-Head and Neck Surgery, School of Medicine, Kyung Hee University) ;
  • Yeo, Seung Geun (Department of Otorhinolaryngology-Head and Neck Surgery, School of Medicine, Kyung Hee University) ;
  • Kim, Sang Hoon (Department of Otorhinolaryngology-Head and Neck Surgery, School of Medicine, Kyung Hee University)
  • 투고 : 2018.08.03
  • 심사 : 2018.11.28
  • 발행 : 2018.12.30

⟨ 이전 논문 다음 논문 ⟩

초록

Granulomatosis with polyangiitis (GPA) and Immunoglobulin (Ig) $G_4$-related disease ($IgG_4$-RD) are rare diseases and early diagnosis and proper management are imperative to prevent multi-organ damage. The authors present a case of a 60 years old woman who had facial paralysis and hearing loss. Lt intact canal wall tympanomastoidectomy, Lt facial nerve decompression and ossiculoplasty with partial ossicular replacement prosthesis (PORP) was done. During operation, middle ear tissue was biopsied and GPA with $IgG_4$-RD was diagnosed. After methyl prednisolone (MPD) pulse therapy and azathioprine therapy, the severity of paralysis was improved. We present this case because common otologic symptoms like facial palsy and hearing loss could be initial symptoms of rare systemic disease.

키워드

참고문헌

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