Archives of Craniofacial Surgery (대한두개안면성형외과학회지)

Korean Cleft Palate-Craniofacial Association (대한두개안면성형외과학회)
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Solitary mastocytoma presenting at birth

  • Ha, Non Hyeon (Department of Plastic and Reconstructive Surgery, Ajou University Hospital) ;
  • Lee, Yoo Jung (Department of Plastic and Reconstructive Surgery, Ajou University Hospital) ;
  • Park, Myong Chul (Department of Plastic and Reconstructive Surgery, Ajou University Hospital) ;
  • Lee, Il Jae (Department of Plastic and Reconstructive Surgery, Ajou University Hospital) ;
  • Kim, Sue Min (Department of Plastic and Reconstructive Surgery, Ajou University Hospital) ;
  • Park, Dong Ha (Department of Plastic and Reconstructive Surgery, Ajou University Hospital)
  • Received : 2017.09.07
  • Accepted : 2018.03.31
  • Published : 2018.06.25
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Abstract

Mastocytosis is a rare disease which occurs in both children and adults, and it can manifest as a solitary or multiple skin lesions. Both can cause cutaneous or systemic symptoms. Because of the heterogeneity of clinical presentation of mastocytosis and its rare prevalence, it can be hard to suspect the mastocytosis at the first time. Most solitary mastocytomas are about 1-5 cm in diameter and have features of brownish-yellow, minimally elevated plaques with a smooth shiny surface. This article presents a case of solitary mastocytoma which occurred in neonate and that we treated through surgical excision. In histopathological examination, it consisted of c-kit-positive mast cells. Although pediatric cutaneous mastocytosis might regress spontaneously, clinicians should keep in mind that it could be associated with systemic mastocytosis which involves hematopoietic system.

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References

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