Journal of the Korean Society of Radiology (대한영상의학회지)

The Korean Society of Radiology (대한영상의학회)
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A Rare Case of Zinner's Syndrome with Ectopic Prostate and Triorchidism

이소성 전립선과 삼중 고환을 가진 Zinner 증후군의 희귀 증례 보고

  • Ko, Ara (Department of Radiology, Chung-Ang University Hosptal) ;
  • Lee, Eun Sun (Department of Radiology, Chung-Ang University Hosptal) ;
  • Park, Hyun Jeong (Department of Radiology, Chung-Ang University Hosptal) ;
  • Lee, Jong Beum (Department of Radiology, Chung-Ang University Hosptal) ;
  • Choi, Byung Ihn (Department of Radiology, Chung-Ang University Hosptal)
  • 고아라 (중앙대학교병원 영상의학과) ;
  • 이은선 (중앙대학교병원 영상의학과) ;
  • 박현정 (중앙대학교병원 영상의학과) ;
  • 이종범 (중앙대학교병원 영상의학과) ;
  • 최병인 (중앙대학교병원 영상의학과)
  • Received : 2017.09.04
  • Accepted : 2017.11.14
  • Published : 2018.05.01
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Abstract

Zinner's syndrome is a rare congenital abnormality of the mesonephric duct. Unilateral renal agenesis, ipsilateral seminal vesicle cyst, and ipsilateral ejaculatory duct obstruction are the triad of maldevelopment of the mesonephric duct which comprises Zinner's syndrome. It is an extremely rare case, in that approximately 100 cases only have been reported worldwide. We discovered a rare developmental anomaly with other mesonephric duct-associated abnormalities, Zinner's syndrome with a presumed ectopic prostate and triorchidism and do report here.

Zinner 증후군은 중간 콩팥 관의 선천적 이상에 의해 생긴 희귀한 증후군이다. 편측 콩팥 무 발생, 동측 정낭낭종, 그리고 동측 사정관 폐쇄가 중간 콩팥관 발생 이상에 의해 생기는 Zinner 증후군의 세 가지 징후이다. 이는 매우 희귀하여 지금까지 전 세계적으로 약 100건 정도가 보고된 바 있다. 이 논문에서 Zinner 증후군과 함께 이소성 전립선, 삼중 고환증을 동반한 것으로 추정되는 매우 드문 증례를 경험하여 보고하고자 한다.

Keywords

References

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