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Minimally Invasive Mitral Valve Repair in a Woman with Marfan Syndrome and Type B Dissection

  • Lim, Mi Hee (Department of Thoracic and Cardiovascular Surgery, Pusan National University Yangsan Hospital, Medical Research Institute of Pusan National University) ;
  • Je, Hyung Gon (Department of Thoracic and Cardiovascular Surgery, Pusan National University Yangsan Hospital, Medical Research Institute of Pusan National University) ;
  • Lee, Sang Kwon (Department of Thoracic and Cardiovascular Surgery, Pusan National University Yangsan Hospital, Medical Research Institute of Pusan National University)
  • Received : 2017.04.12
  • Accepted : 2017.06.26
  • Published : 2018.02.05

Abstract

We report the case of a patient with mitral regurgitation complicated by type B dissection and Marfan syndrome (MFS) who was managed successfully with minimally invasive mitral valve repair. Without type A aortic dissection or aortic root dilation, MFS patients may develop mitral valve regurgitation, as in this case, and need valve surgery to improve their symptoms and long-term survival. However, it is not clear that a full sternotomy and prophylactic aortic surgery are necessary. Although retrograde perfusion to the dissected aorta is controversial, our approach minimizes the risk of future anticipated aortic surgery in MFS patients.

Keywords

References

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Cited by

  1. An Endoscopic Solution to Mitral Regurgitation in a Complex Patient With Marfan Syndrome vol.14, pp.6, 2018, https://doi.org/10.1177/1556984519874799