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Large Atrial Septal Defect Closure in a Patient with Severe Pulmonary Arterial Hypertension

  • Supomo, Supomo (Thoracic and Cardiovascular Surgery Division, Department of Surgery, Dr. Sardjito General Hospital, Universitas Gadjah Mada) ;
  • Hartopo, Anggoro Budi (Department of Cardiology and Vascular Medicine, Dr. Sardjito General Hospital, Universitas Gadjah Mada) ;
  • Anggrahini, Dyah Wulan (Department of Cardiology and Vascular Medicine, Dr. Sardjito General Hospital, Universitas Gadjah Mada) ;
  • Darmawan, Handy (Thoracic and Cardiovascular Surgery Division, Department of Surgery, Dr. Sardjito General Hospital, Universitas Gadjah Mada) ;
  • Dinarti, Lucia Kris (Department of Cardiology and Vascular Medicine, Dr. Sardjito General Hospital, Universitas Gadjah Mada)
  • Received : 2017.04.12
  • Accepted : 2017.06.13
  • Published : 2017.10.05

Abstract

Patients with an atrial septal defect (ASD) and severe pulmonary arterial hypertension (PAH) are considered ineligible for defect closure surgery because of the risk of right ventricular decompensation and death after the operation. We report the case of a patient with large ASD and severe PAH who was able to undergo defect closure surgery successfully following long-term use of combined oral sildenafil and beraprost.

Keywords

References

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