대한두개안면성형외과학회지 (Archives of Craniofacial Surgery)

  • 제18권3호
  • /
  • Pages.166-171
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  • 2017
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  • 2287-1152(pISSN)
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  • 2287-5603(eISSN)
대한두개안면성형외과학회 (Korean Cleft Palate-Craniofacial Association)
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Surgical Management of Localized Scleroderma

  • Lee, Jae Hyun (Department of Plastic and Reconstructive Surgery, Hanyang University College of Medicine) ;
  • Lim, Soo Yeon (Department of Plastic and Reconstructive Surgery, Hanyang University College of Medicine) ;
  • Lee, Jang Hyun (Department of Plastic and Reconstructive Surgery, Hanyang University Guri Hospital, Hanyang University College of Medicine) ;
  • Ahn, Hee Chang (Department of Plastic and Reconstructive Surgery, Hanyang University College of Medicine)
  • 투고 : 2017.08.16
  • 심사 : 2017.09.08
  • 발행 : 2017.09.20
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초록

Background: Localized scleroderma is characterized by a thickening of the skin from excessive collagen deposits. It is not a fatal disease, but quality of life can be adversely affected due to changes in skin appearance, joint contractures, and, rarely, serious deformities of the face and extremities. We present six cases of localized scleroderma in face from our surgical practice. Methods: We reviewed six localized scleroderma cases that were initially treated with medication and then received follow-up surgery between April 2003 and February 2015. Six patients had facial lesions. These cases presented with linear dermal sclerosis on the forehead, oval subcutaneous and dermal depression in the cheek. Results: En coup de sabre (n=4), and oval-shaped lesion of the face (n=2) were successfully treated. Surgical methods included resection with or without Z-plasty (n=3), fat graft (n=1), dermofat graft (n=1), and adipofascial free flap (n=1). Deformities of the affected parts were surgically corrected without reoccurrence. Conclusion: We retrospectively reviewed six cases of localized scleroderma that were successfully treated with surgery. And we propose an algorithm for selecting the best surgical approach for individual localized scleroderma cases. Although our cases were limited in number and long-term follow-up will be necessary, we suggest that surgical management should be considered as an option for treating scleroderma patients.

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참고문헌

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피인용 문헌

  1. Overview of Juvenile localized scleroderma and its management vol.16, pp.1, 2020, https://doi.org/10.1007/s12519-019-00320-9
  2. Treatment of linear scleroderma “En coup de Sabre” with single‐stage autologous fat grafting: A case report and review of the literature vol.20, pp.1, 2021, https://doi.org/10.1111/jocd.13490
  3. A pilot study on ex vivo expanded autologous adipose‐derived stem cells of improving fat retention in localized scleroderma patients vol.10, pp.8, 2021, https://doi.org/10.1002/sctm.20-0419
  4. Aesthetic and therapeutic outcome of fat grafting for localized Scleroderma treatment: From basic study to clinical application vol.20, pp.9, 2017, https://doi.org/10.1111/jocd.13941