Journal of Cardiovascular Imaging

Korean Society of Echocardiography (한국심초음파학회)
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Severe Aortic Stenosis Associated with Unicommissural Unicuspid Aortic Valve in a Middle Aged Male

  • Kwon, Hee-Jin (Division of Cardiology, Department of Internal Medicine, School of Medicine, Chungnam National University, Chungnam National University Hospital) ;
  • Park, Jae-Hyeong (Division of Cardiology, Department of Internal Medicine, School of Medicine, Chungnam National University, Chungnam National University Hospital) ;
  • Kim, Song Soo (Department of Diagnostic Imaging, School of Medicine, Chungnam National University, Chungnam National University Hospital) ;
  • Sun, Byung Joo (Division of Cardiology, Department of Internal Medicine, School of Medicine, Chungnam National University, Chungnam National University Hospital) ;
  • Jin, Sun Ah (Division of Cardiology, Department of Internal Medicine, School of Medicine, Chungnam National University, Chungnam National University Hospital) ;
  • Kim, Jun-Hyung (Division of Cardiology, Department of Internal Medicine, School of Medicine, Chungnam National University, Chungnam National University Hospital) ;
  • Lee, Jae-Hwan (Division of Cardiology, Department of Internal Medicine, School of Medicine, Chungnam National University, Chungnam National University Hospital) ;
  • Choi, Siwan (Division of Cardiology, Department of Internal Medicine, School of Medicine, Chungnam National University, Chungnam National University Hospital) ;
  • Jeong, Jin-Ok (Division of Cardiology, Department of Internal Medicine, School of Medicine, Chungnam National University, Chungnam National University Hospital) ;
  • Seong, In-Whan (Division of Cardiology, Department of Internal Medicine, School of Medicine, Chungnam National University, Chungnam National University Hospital)
  • Received : 2016.04.02
  • Accepted : 2016.07.26
  • Published : 2016.09.27
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Abstract

Unicuspid aortic valve (UAV) is an extremely rare form of congenital aortic valvular abnormality. Although UAV shows similar clinical characteristics to bicuspid aortic valve, the clinical symptoms develop at earlier age and progress at a faster pace in UAV. In this report, we are presenting a 42-year-old male with severe aortic stenosis associated with unicommissural UAV. The patients underwent a successful Bentall operation.

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References

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