Korean Circulation Journal

The Korean Society of Cardiology (대한심장학회)
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Congenital Absence of Superior Vena Cava with No Manifestation of Superior Vena Cava Syndrome

  • Park, Chan Soon (Cardiovascular Center, Seoul National University Bundang Hospital) ;
  • Kim, Jeong Jae (Department of Radiology, Seoul National University Bundang Hostpial) ;
  • Park, Jin Joo (Cardiovascular Center, Seoul National University Bundang Hospital)
  • Received : 2015.12.17
  • Accepted : 2016.03.24
  • Published : 2016.09.30
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Abstract

Total absence of superior vena cava (SVC) is a very rare anomaly, and the patient usually suffers from SVC syndrome or conduction disturbances. We report an asymptomatic 27 year-old male, with complete absence of SVC. Transthoracic echocardiography and computed tomography demonstrated the absence of SVC and other congenital cardiac anomalies, but the presence of prominent collateral vessels that allow a sufficient venous return.

Keywords

References

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Cited by

  1. Venous Collateral Pathways in Superior Thoracic Inlet Obstruction: A Systematic Analysis of Anatomy, Embryology, and Resulting Patterns vol.213, pp.1, 2016, https://doi.org/10.2214/ajr.18.20172