Journal of Dental Anesthesia and Pain Medicine

The Korean Dental Society of Anesthsiology (대한치과마취과학회)
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Perioperative airway management of a patient with Beckwith-Wiedemann syndrome

  • Tsukamoto, Masanori (Department of Dental Anesthesiology, Kyushu University Hospital) ;
  • Hitosugi, Takashi (Department of Dental Anesthesiology, Faculty of Dental Science, Kyushu University) ;
  • Yokoyama, Takeshi (Department of Dental Anesthesiology, Faculty of Dental Science, Kyushu University)
  • Received : 2016.12.15
  • Accepted : 2016.12.26
  • Published : 2016.12.31
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Abstract

Airway obstruction in pediatric patients always poses a challenge for anesthesiologists. Beckwith-Wiedemann syndrome causes various abnormalities such as macroglossia and omphalocele. Patients with these abnormalities often need corrective surgeries. Management of difficult airway caused by conditions such as macroglossia in patients with this syndrome could be challenging. We encountered a case of difficult airway in an infant with Beckwith-Wiedemann syndrome. It was predicted that macroglossia might cause difficult ventilation, intubation, and extubation. Preoperative assessment and preparations for difficult airway should be considered.

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References

  1. Kim Y, Shibutani T, Hirota Y, Mahbub SF, Matsuura H. Anesthetic considerations of two sisters with Beckwith-Wiedemann syndrome. Anesth Prog 1996; 43: 24-8.
  2. Tobias JD, Lowe S, Holcomb GW 3rd. Anesthetic considerations of an infant with Beckwith-Wiedemann syndrome. J Clin Anesth 1992; 4: 484-6. https://doi.org/10.1016/0952-8180(92)90224-O
  3. Batra M, Valecha UK. Anesthetic management of tongue reduction in a case of Beckwith-Wiedemann syndrome. J Anaesthesiol Clin Pharmacol 2014; 30: 562-4. https://doi.org/10.4103/0970-9185.142863
  4. Suan C, Ojeda R, Garcia-Perla JL, Perez-Torres MC. Anaesthesia and the Beckwith-Wiedemann syndrome. Paediatr Anaesth 1996; 6: 231-3. https://doi.org/10.1111/j.1460-9592.1996.tb00435.x
  5. Celiker V, Basgul E, Karagoz AH. Anesthesia in Beckwith-Wiedemann syndrome. Paediatr Anaesth 2004; 14: 778-80. https://doi.org/10.1111/j.1460-9592.2004.01283.x
  6. Channabasapa SM, Pradeep SH, Dharmapa S, Sarji D. Anesthetic management of a neonate with Beckwith-Wiedemann syndrome posted for repair of exomphalos. Saudi J Anaesth 2016; 10: 249-50. https://doi.org/10.4103/1658-354X.169490
  7. Kimura Y, Kamada Y, Kimura S. Anesthetic management of two cases of Beckwith-Wiedemann syndrome. J Anesth 2008; 22: 93-5. https://doi.org/10.1007/s00540-007-0571-5
  8. Gurkowski MA, Rasch DK. Anesthetic considerations for Beckwith-Wiedemann syndrome, Anesthesiology 1989; 70: 711-2. https://doi.org/10.1097/00000542-198904000-00031
  9. Greenspun JC, Hannallah RS, Welborn LG, Norden JM. Comparison of sevoflurane and halothane anesthesia in children undergoing outpatient ear, nose, and throat surgery. J Clin Anesth 1995; 7: 398-402. https://doi.org/10.1016/0952-8180(95)00071-O
  10. Okutani R, Arima Y, Oda Y. Anesthetic management in a child with Rolland-Desbuquois type dyssegmental dysplasia. J Clin Anesth 2014; 26: 676-8. https://doi.org/10.1016/j.jclinane.2014.06.004
  11. Priebe HJ. Should anesthesiologists have to confirm effective facemask ventilation before administering the muscle relaxant?. J Anesth 2016; 30: 132-7. https://doi.org/10.1007/s00540-015-2072-2
  12. Kadouch DJ, Maas SM, Dubois L, van der Horst CM. Surgical treatment of macroglossia in patients with Beckwith-Wiedemann syndrome: a 20-year experience and review of the literature. Int J Oral Maxillofac Surg 2012; 41: 300-8. https://doi.org/10.1016/j.ijom.2011.10.021
  13. Kittur MA, Padgett J, Drake D. Management of macroglossia in Beckwith-Wiedemann syndrome. Br J Oral Maxillofac Surg 2013; 51: 6-8. https://doi.org/10.1016/j.bjoms.2012.03.025

Cited by

  1. The Prevalence of Difficult Airway in Children With Beckwith-Wiedemann Syndrome: A Retrospective Cohort Study vol.133, pp.6, 2016, https://doi.org/10.1213/ane.0000000000005536