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DOUBLE CHAMBERED RIGHT VENTRICLE WITH VENTRICULAR SEPTAL DEFECT IN ADULTS: CASE SERIES AND REVIEW OF THE LITERATURE

  • MOUSTAFA, SHERIF (DIVISION OF CARDIOVASCULAR DISEASES, MAYO CLINIC ARIZONA) ;
  • PATTON, DAVID J. (SECTION OF PEDIATRIC CARDIOLOGY, UNIVERSITY OF CALGARY) ;
  • ALVAREZ, NANETTE (DIVISION OF CARDIOVASCULAR DISEASES, UNIVERSITY OF CALGARY) ;
  • AL SHANAWANI, MANSOUR (DEPARTMENT OF RADIOLOGY, KING FAHAD MEDICAL CITY) ;
  • ALDOSSARI, KHALID (DEPARTMENT OF RADIOLOGY, KING FAHAD MEDICAL CITY) ;
  • CONNELLY, MICHAEL S. (DIVISION OF CARDIOVASCULAR DISEASES, UNIVERSITY OF CALGARY) ;
  • PRIEUR, TIMOTHY (DIVISION OF CARDIOVASCULAR DISEASES, UNIVERSITY OF CALGARY) ;
  • MOOKADAM, FAROUK (DIVISION OF CARDIOVASCULAR DISEASES, MAYO CLINIC ARIZONA)
  • Received : 2014.08.12
  • Accepted : 2015.02.27
  • Published : 2015.03.27

Abstract

Double-chambered right ventricle (DCRV) is an uncommon congenital anomaly in which anomalous muscle bands divide the right ventricle into two chambers; a proximal high-pressure and distal low-pressure chamber. It may be associated with mid right ventricular obstruction. It is commonly associated with other congenital anomalies, most frequently perimembranous ventricular septal defect (PM-VSD). We herein present 5 adult patients with concomitant DCRV and PM-VSD who varied in their symptomatic presentations and the ways of management.

Keywords

References

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