Tuberculosis and Respiratory Diseases

The Korean Academy of Tuberculosis and Respiratory Diseases (대한결핵및호흡기학회)
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A Case of Solitary Fibrous Pleura Tumor Associated with Severe Hypoglycemia: Doege-Potter Syndrome

  • Jang, Jong Geol (Department of Internal Medicine, Regional Center for Respiratory Disease, Yeungnam University Medical Center, Yeungnam University College of Medicine) ;
  • Chung, Jin Hong (Department of Internal Medicine, Regional Center for Respiratory Disease, Yeungnam University Medical Center, Yeungnam University College of Medicine) ;
  • Hong, Kyung Soo (Department of Internal Medicine, Regional Center for Respiratory Disease, Yeungnam University Medical Center, Yeungnam University College of Medicine) ;
  • Ahn, June Hong (Department of Internal Medicine, Regional Center for Respiratory Disease, Yeungnam University Medical Center, Yeungnam University College of Medicine) ;
  • Lee, Jae Young (Department of Internal Medicine, Regional Center for Respiratory Disease, Yeungnam University Medical Center, Yeungnam University College of Medicine) ;
  • Jo, Jae Ho (Department of Internal Medicine, Regional Center for Respiratory Disease, Yeungnam University Medical Center, Yeungnam University College of Medicine) ;
  • Lee, Dong Won (Department of Internal Medicine, Regional Center for Respiratory Disease, Yeungnam University Medical Center, Yeungnam University College of Medicine) ;
  • Shin, Kyeong Cheol (Department of Internal Medicine, Regional Center for Respiratory Disease, Yeungnam University Medical Center, Yeungnam University College of Medicine) ;
  • Lee, Kwan Ho (Department of Internal Medicine, Regional Center for Respiratory Disease, Yeungnam University Medical Center, Yeungnam University College of Medicine) ;
  • Kim, Mi Jin (Department of Pathology, Regional Center for Respiratory Disease, Yeungnam University Medical Center, Yeungnam University College of Medicine) ;
  • Lee, Jung Cheul (Department of Thoracic and Cardiovascular Surgery, Regional Center for Respiratory Disease, Yeungnam University Medical Center, Yeungnam University College of Medicine) ;
  • Lee, Jang Hoon (Department of Thoracic and Cardiovascular Surgery, Regional Center for Respiratory Disease, Yeungnam University Medical Center, Yeungnam University College of Medicine) ;
  • Lee, Jae Kyo (Department of Radiology, Regional Center for Respiratory Disease, Yeungnam University Medical Center, Yeungnam University College of Medicine)
  • Received : 2014.07.16
  • Accepted : 2014.12.11
  • Published : 2015.02.28
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Abstract

Solitary fibrous tumor of the pleura (SFTP) is a rare primary intrathoracic tumor that arises from mesenchymal tissue underlying the mesothelial layer of the pleura. It usually has an indolent clinical course. The hypoglycemia that accompanies SFTP was first described by Doege and Potter independently in 1930, hence the eponym Doege-Potter syndrome (DPS). The incidence of DPS is reported to be ~4%. In this report, we present a typical case of DPS that was cured through complete surgical resection.

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References

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