Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
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A Successfully Treated Case of Gorham-Stout Syndrome with Sternal Involvement

  • Kim, Bong Jun (Department of Thoracic and Cardiovascular Surgery, Gangnam Severance Hospital, Yonsei University College of Medicine) ;
  • Kim, Tae Hoon (Department of Thoracic and Cardiovascular Surgery, Gangnam Severance Hospital, Yonsei University College of Medicine) ;
  • Kim, Do Jung (Department of Thoracic and Cardiovascular Surgery, Gangnam Severance Hospital, Yonsei University College of Medicine) ;
  • Noh, Dongsub (Department of Thoracic and Cardiovascular Surgery, Gangnam Severance Hospital, Yonsei University College of Medicine) ;
  • Haam, Seok Jin (Department of Thoracic and Cardiovascular Surgery, Gangnam Severance Hospital, Yonsei University College of Medicine) ;
  • Lee, Sungsoo (Department of Thoracic and Cardiovascular Surgery, Gangnam Severance Hospital, Yonsei University College of Medicine)
  • Received : 2014.04.28
  • Accepted : 2014.10.27
  • Published : 2015.02.05
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Abstract

Gorham-Stout Syndrome (GSS) is a rare disease characterized by localized bone resorption. Any part of the skeleton may be affected; therefore, symptoms can vary depending on the site involved. Pathological analysis reveals lymphovascular proliferation and osteolysis in the affected lesion, but the etiology of the disease is poorly understood. When GSS occurs in the chest, chylothorax or respiratory failure may occur. Thus far, a standard treatment for GSS has not been established, and the prognosis remains unknown. The following case report describes a successfully treated case of GSS in a 16-year-old boy with an affected sternum and ribs.

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References

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  2. A rare case of Gorham-stout syndrome involving the thoracic spine with progressive bilateral chylothorax: a case report vol.20, pp.None, 2015, https://doi.org/10.1186/s12891-019-2542-z
  3. A Case of Vanishing Bones vol.41, pp.11, 2015, https://doi.org/10.1542/pir.2018-0297
  4. Gorham-Stout Disease in a Middle-Aged Patient Treated by Posterior Lateral Fusion: A Case Report and Literature Review vol.7, pp.2, 2021, https://doi.org/10.21129/nerve.2021.7.2.106