Korean Journal of Radiology

The Korean Society of Radiology (대한영상의학회)
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A Rare Case of Diffuse Pulmonary Lymphangiomatosis in a Middle-Aged Woman

  • Lim, Hyun-Ju (Department of Radiology and Center for Imaging, Samsung Medical Center, Sungkyunkwan University Schoolof Medicine) ;
  • Han, Joungho (Department of Pathology, Samsung Medical Center, Sungkyunkwan University Schoolof Medicine) ;
  • Kim, Hong Kwan (Department of Thoracic Surgery, Samsung Medical Center, Sungkyunkwan University Schoolof Medicine) ;
  • Kim, Tae Sung (Department of Radiology and Center for Imaging, Samsung Medical Center, Sungkyunkwan University Schoolof Medicine)
  • Received : 2013.01.03
  • Accepted : 2013.12.13
  • Published : 2014.04.01
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Abstract

Diffuse pulmonary lymphangiomatosis (DPL) is a rare lymphatic disorder characterized by lymphatic channel proliferation. It is mostly reported in children and young adults. Here, we report a case involving a 52-year-old asymptomatic woman who presented with increased interstitial markings, as seen on a chest radiograph. Diffuse interstitial septal thickening was found on a serial follow-up chest computed tomography scan, and lymphangitic metastasis was the primary radiologic differential diagnosis. However, histologic sections of wedge resected lung revealed diffuse pleural and interlobular septal lymphatic proliferation characteristic of DPL.

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References

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