The Korean Journal of Medicine

  • 제86권5호
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  • Pages.651-654
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  • 2014
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  • 1738-9364(pISSN)
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  • 2289-0769(eISSN)
대한내과학회 (The Korean Association of Internal Medicine)
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전신홍반루푸스의 비장경색으로 처음 발현된 항인지질 증후군 1예

Splenic Infarction as the Initial Manifestation of Antiphospholipid Syndrome in a Systemic Lupus Erythematosus Patient

  • 정혜윤 (차의과학대학교 분당차병원 내과) ;
  • 강산하 (차의과학대학교 분당차병원 내과) ;
  • 송지현 (차의과학대학교 분당차병원 내과) ;
  • 신선영 (차의과학대학교 분당차병원 내과) ;
  • 민다니엘 (차의과학대학교 분당차병원 내과) ;
  • 한규현 (차의과학대학교 분당차병원 내과) ;
  • 최진정 (차의과학대학교 분당차병원 내과)
  • Jeong, Hye Yun (Division of Rheumatology, Department of Internal Medicine, Bundang CHA Medical Center, CHA University) ;
  • Kang, San Ha (Division of Rheumatology, Department of Internal Medicine, Bundang CHA Medical Center, CHA University) ;
  • Song, Ji Hyun (Division of Rheumatology, Department of Internal Medicine, Bundang CHA Medical Center, CHA University) ;
  • Shin, Sun Young (Division of Rheumatology, Department of Internal Medicine, Bundang CHA Medical Center, CHA University) ;
  • Min, Daniel (Division of Rheumatology, Department of Internal Medicine, Bundang CHA Medical Center, CHA University) ;
  • Han, Kyu Hyun (Division of Rheumatology, Department of Internal Medicine, Bundang CHA Medical Center, CHA University) ;
  • Choi, Jin Jung (Division of Rheumatology, Department of Internal Medicine, Bundang CHA Medical Center, CHA University)
  • 투고 : 2013.06.25
  • 심사 : 2013.10.16
  • 발행 : 2014.05.01
⟨ 이전 논문 다음 논문 ⟩

초록

좌상복부 통증을 호소하는 전신홍반루푸스 환자에서 항인지질 항체 양성 소견과 함께 비장경색이 단독으로 발생된 증례로 혈전증의 다른 위험 요인을 배제한 후 항인지질 항체 증후군으로 진단한 1예를 경험하였기에 보고하는 바이다.

Systemic lupus erythematosus (SLE) is a multisystem autoimmune disease. In patients with SLE, the prevalence of antiphospholipid antibodies is considerably higher, and is largely responsible for thrombosis. Splenic infarction is a rare complication of arterial thrombosis in patients with SLE. It is important to consider splenic infarction in a patient with SLE complaining of left upper quadrant (LUQ) pain because of the possibility of severe infarction-related complications, such as subcapsular hemorrhage and splenic rupture. We report a case of solitary splenic infarction in a patient with SLE. The only symptom was LUQ pain of 3-day duration. Lupus anticoagulant activity was positive and abdominal-pelvic computed tomography (CT) was consistent with splenic infarction. She did not show any other evidence of thrombotic events. The patient was diagnosed with antiphospholipid syndrome that presented as a splenic infarction in a SLE patient.

키워드

참고문헌

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