The Korean Journal of Medicine

  • 제86권5호
  • /
  • Pages.603-607
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  • 2014
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  • 1738-9364(pISSN)
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  • 2289-0769(eISSN)
대한내과학회 (The Korean Association of Internal Medicine)
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바터팽대부에 점막하 종양으로 보인 신경절세포 부신경절종 1예

A Gangliocytic Paraganglioma Presenting as a Submucosal Tumor in the Ampulla

  • 양재훈 (건국대학교 의과대학 내과학교실) ;
  • 천영국 (건국대학교 의과대학 내과학교실) ;
  • 이태윤 (건국대학교 의과대학 내과학교실) ;
  • 심찬섭 (건국대학교 의과대학 내과학교실) ;
  • 김욱연 (건국대학교 의과대학 병리학교실)
  • Yang, Jae Hoon (Department of Internal Medicine, Konkuk University School of Medicine) ;
  • Cheon, Young Koog (Department of Internal Medicine, Konkuk University School of Medicine) ;
  • Lee, Tae Yoon (Department of Internal Medicine, Konkuk University School of Medicine) ;
  • Shim, Chan Sup (Department of Internal Medicine, Konkuk University School of Medicine) ;
  • Kim, Wook Youn (Department of Pathology, Konkuk University School of Medicine)
  • 투고 : 2013.08.26
  • 심사 : 2013.10.28
  • 발행 : 2014.05.01
⟨ 이전 논문 다음 논문 ⟩

초록

신경절세포 부신경절종은 드물게 발생하는 신경내분비종양으로 양성 질환으로 간주되어 왔다. 그러나 림프절전이나 기타 타 장기로의 원격전이가 확인된 예도 보고되고 있어 반드시 원격전이 가능성을 고려해야 한다. 신경절세포 부신경절종은 내시경 소견만으로는 진단이 어렵고 결국 조직학적 진단이 반드시 필요하다. 최근 저자들은 내시경 유두부 절제술 후 2년 동안 재발을 보이지 않는 점막하 종양 형태를 가진 신경절세포 부신경절종 1예를 문헌고찰과 함께 보고하는 바이다.

A gangliocytic paraganglioma (GP) is a rare benign neuroendocrine tumor. However, its origin remains unclear. It is seen most frequently in the second portion of the duodenum. At endoscopy, a GP characteristically appears as a pedunculated nodular submucosal tumor with erosions and surface ulcers. The histological diagnosis is usually made from endoscopic biopsies showing the presence of epithelioid, spindle, and ganglion cells. We experienced a case of GP in a 38-year-old female who was referred because of a possible ampullary tumor. The endoscopic images showed a 1.5-cm, oval ampullary tumor covered with normal mucosa. An endoscopic biopsy showed chronic duodenitis. The tumor was removed by an endoscopic papillectomy. We report a case of duodenal GP that presented as a submucosal tumor that was treated with a papillectomy and review the literature.

키워드

참고문헌

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