Korean Journal of Head & Neck Oncology (대한두경부종양학회지)

The Korean Society for Head and Neck Oncology (대한두경부종양학회)
권호 표지

A Case of Embryonal Rhabdomyosarcoma at Left Parotid Gland in 8-Month-Old Infant

8개월 영아의 좌측 이하선 부위에서 발생한 배아형 횡문근육종 1예

  • Cho, Minhyuk (Department of Otolaryngology, School of Medicine, Ajou University) ;
  • Kim, Yeon Soo (Department of Otolaryngology, School of Medicine, Ajou University) ;
  • Shin, YooSeob (Department of Otolaryngology, School of Medicine, Ajou University) ;
  • Kim, Chul-Ho (Department of Otolaryngology, School of Medicine, Ajou University)
  • 조민혁 (아주대학교 의과대학 이비인후과학교실) ;
  • 김연수 (아주대학교 의과대학 이비인후과학교실) ;
  • 신유섭 (아주대학교 의과대학 이비인후과학교실) ;
  • 김철호 (아주대학교 의과대학 이비인후과학교실)
  • Received : 2014.10.14
  • Accepted : 2014.10.17
  • Published : 2014.10.31
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Abstract

Rhabdomyosarcoma is the most common sarcoma in children less than 15 years of age. Two major histological subtypes are embryonal and alveolar. Embryonal rhabdomyosarcoma is diagnosed by immunopathology and treatments require coordinated management plans that include surgery, chemotherapy, and usually radiotherapy. 8-month-old male infant visited with swelling in left parotid area. Computed tomography scan showed a heterogeneous mass in the left parotid area and the result of fine-needle aspiration cytology was suspicious malignancy. Left total parotidectomy was performed and CSF leakage was noted and repaired. Confirmed by positive reactions to desmin and myogenin, the diagnosis was embryonal rhabdomyosarcoma. On postoperative brain MRI, extension along the meninges was noted and for treatment, chemotherapy and gamma knife radiosurgery were done. Five years after initial surgical resection(3 years and 10 months after completion of chemotherapy and gamma knife radiosurgery), the child did not show any evidence of local recurrence or distant metastasis.

Keywords

References

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