Radiation Oncology Journal

The Korean Society for Radiation Oncology (대한방사선종양학회)
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Aggressive clinical course of extramammary Paget disease after radiotherapy

  • Choi, Yunseon (Department of Radiation Oncology, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Park, Won (Department of Radiation Oncology, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Lee, Jeeyun (Department of Hematology and Oncology, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Cho, Eun Yoon (Department of Pathology, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Moon, Goo-Hyun (Department of Plastic Surgery, Samsung Medical Center, Sungkyunkwan University School of Medicine)
  • Received : 2014.03.26
  • Accepted : 2014.05.07
  • Published : 2014.06.30
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Abstract

Extramammary Paget disease (EMPD) is a rare disease, especially in Asian populations. Surgical resection is considered the primary treatment option. Recently, radiotherapy has been suggested as an EMPD treatment, either as an alternative to surgical resection or in combination with surgical resection. This report reviewed a patient with EMPD who was treated with wide excision of the EMPD site followed by radiotherapy for remaining gross lymph node metastases. The aim of this report was to determine the optimal treatment for advanced EMPD.

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References

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  1. Primary extramammary invasive Paget’s vulvar disease: what is the standard, what are the challenges and what is the future for radiotherapy? vol.16, pp.None, 2014, https://doi.org/10.1186/s12885-016-2622-5