Imaging Science in Dentistry

Korean Academy of Oral and Maxillofacial Radiology (대한영상치의학회)
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A unique case of Turner syndrome accompanying prolactinoma and unexpected elongated styloid process: Clinical and cone-beam computed tomographic features

  • Evlice, Burcu (Department of Oral and Maxillofacial Radiology, Faculty of Dentistry, Cukurova University) ;
  • Tatli, Ufuk (Department of Oral and Maxillofacial Surgery, Faculty of Dentistry, Cukurova University) ;
  • Yazicioglu, Iffet (Department of Pediatric Dentistry, Faculty of Dentistry, Cukurova University) ;
  • Evlice, Ahmet (Department of Neurology, Faculty of Medicine, Cukurova University) ;
  • Oztunc, Haluk (Department of Oral and Maxillofacial Radiology, Faculty of Dentistry, Cukurova University)
  • Received : 2012.11.26
  • Accepted : 2013.01.18
  • Published : 2013.06.30
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Abstract

Turner syndrome (TS) is one of the most common chromosomal abnormalities, with an estimated frequency among female live births of 1/2,000-3,000. The syndrome is characterized by the partial or complete absence of one X chromosome (45,X karyotype). We reported a unique case of a 40-year-old woman with TS accompanying unexpected elongated styloid process specific to Eagle syndrome (ES) and followed up-prolactinoma. The present article is the first report to define the cone-beam computed tomographic (CBCT) features of TS accompanying ES. Patients with TS carry various risks that make treatment more complicated; thus advanced imaging techniques for proper treatment and follow-up are extremely important. In the light of CBCT examination, craniofacial abnormalities specific to TS and accompanying syndromes such as the crowding of teeth especially in the maxillary anterior region caused by maxillary narrowness, micrognatic maxilla and mandible, relative mandibular retrusion, malocclusion, open-bite, and an elongated styloid process (length of 32.7 mm) on the right side were illustrated in detail.

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References

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