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성인에서 진단된 영아 간혈관내피종 1예

Infantile Hepatic Hemangioendothelioma in an Adult

  • 방기배 (성균관대학교 의과대학 강북삼성병원 내과) ;
  • 조용균 (성균관대학교 의과대학 강북삼성병원 내과) ;
  • 이상혁 (성균관대학교 의과대학 강북삼성병원 내과) ;
  • 박은혜 (성균관대학교 의과대학 강북삼성병원 내과) ;
  • 설지수 (성균관대학교 의과대학 강북삼성병원 내과) ;
  • 채승완 (성균관대학교 의과대학 강북삼성병원 내과) ;
  • 조상원 (성균관대학교 의과대학 강북삼성병원 내과)
  • Bang, Ki Bae (Department of Internal Medicine, Kangbuk Samsung Hospital, Sungkyunkwan University School of Medicine) ;
  • Cho, Yong Kyun (Department of Internal Medicine, Kangbuk Samsung Hospital, Sungkyunkwan University School of Medicine) ;
  • Lee, Sang Hyuk (Department of Internal Medicine, Kangbuk Samsung Hospital, Sungkyunkwan University School of Medicine) ;
  • Park, Eun Hye (Department of Internal Medicine, Kangbuk Samsung Hospital, Sungkyunkwan University School of Medicine) ;
  • Seol, Ji Soo (Department of Internal Medicine, Kangbuk Samsung Hospital, Sungkyunkwan University School of Medicine) ;
  • Chae, Seoung Wan (Department of Internal Medicine, Kangbuk Samsung Hospital, Sungkyunkwan University School of Medicine) ;
  • Jo, Sang Won (Department of Internal Medicine, Kangbuk Samsung Hospital, Sungkyunkwan University School of Medicine)
  • 투고 : 2012.06.14
  • 심사 : 2012.07.13
  • 발행 : 2013.02.01

초록

영아 간혈관내피종은 양성 혈관 질환으로 성인에서 진단되는 경우는 매우 드물다. 저자들은 일반적인 종양의 자연경과와 달리 69세 성인에서 진단된 영아 간혈관내피종을 경험하였으며 이에 대한 국내보고가 없어 문헌고찰과 함께 보고하는 바이다.

Infantile hepatic hemangioendothelioma is a rare disorder. It is a benign entity and usually resolves spontaneously. Most patients present in infancy and early childhood. Because of its natural course and symptom onset, most cases are discovered during childhood. We experienced a rare case of infantile hepatic hemangioendothelioma in an adult.

키워드

참고문헌

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