The Korean Journal of Medicine

The Korean Association of Internal Medicine (대한내과학회)
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Pericardial Amyloidosis Associated with Light-chain Myeloma

가벼운 사슬 골수종과 동반된 심장막 아밀로이드증

  • Chang, Je Ho (Department of Internal Medicine, Inje University Ilsan Paik Hospital) ;
  • Chang, Sun Hee (Department of Pathology, Inje University Ilsan Paik Hospital) ;
  • Huh, Jin Won (Department of Internal Medicine, Inje University Ilsan Paik Hospital) ;
  • Lee, Sung Yun (Department of Internal Medicine, Inje University Ilsan Paik Hospital) ;
  • Kim, Jung A (Department of Internal Medicine, Inje University Ilsan Paik Hospital) ;
  • Yoon, Seong Min (Department of Internal Medicine, Inje University Ilsan Paik Hospital) ;
  • Lee, Hye Ran (Department of Internal Medicine, Inje University Ilsan Paik Hospital)
  • 장재호 (인제대학교 일산백병원 내과학교실) ;
  • 장선희 (인제대학교 일산백병원 병리과교실) ;
  • 허진원 (인제대학교 일산백병원 내과학교실) ;
  • 이성윤 (인제대학교 일산백병원 내과학교실) ;
  • 김정아 (인제대학교 일산백병원 내과학교실) ;
  • 윤성민 (인제대학교 일산백병원 내과학교실) ;
  • 이혜란 (인제대학교 일산백병원 내과학교실)
  • Received : 2008.07.01
  • Accepted : 2008.09.02
  • Published : 2013.05.01
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Abstract

Amyloidosis is characterized by the deposition of amyloid fibrils, which cause both functional and structural damage to organs. Cardiac involvement with amyloids is a common cause of secondary cardiomyopathy and leads to congestive heart failure. Pericardial amyloidosis usually occurs at the late or terminal stage of the disease after myocardial involvement, but it is extremely rare for pericardial amyloidosis to proceed with myocardial involvement. Here, we report a rare case of a 66-year-old patient with light-chain myeloma, who presented with pericardial effusion but no evidence of cardiomyopathy.

Keywords

References

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