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Encapsulating Peritoneal Sclerosis Occurring in a Hemodialysis Patient

혈액 투석 환자에서 발생한 경화성 피막성 복막염 1예

  • Song, Yun A (Department of Internal Medicine, GangNeung Asan Hospital, University of Ulsan College of Medicine) ;
  • Kim, Eun Jung (Department of Internal Medicine, GangNeung Asan Hospital, University of Ulsan College of Medicine) ;
  • Kwon, Jun Sung (Department of Internal Medicine, GangNeung Asan Hospital, University of Ulsan College of Medicine) ;
  • Kim, Su Hee (Department of Internal Medicine, GangNeung Asan Hospital, University of Ulsan College of Medicine) ;
  • Choi, Kun Moo (Department of General Surgery, GangNeung Asan Hospital, University of Ulsan College of Medicine) ;
  • Eom, Dae Woon (Department of Patholgy, GangNeung Asan Hospital, University of Ulsan College of Medicine) ;
  • Song, Kyung Il (Department of Internal Medicine, GangNeung Asan Hospital, University of Ulsan College of Medicine)
  • 송윤아 (울산대학교 의과대학 강릉아산병원 내과) ;
  • 김은정 (울산대학교 의과대학 강릉아산병원 내과) ;
  • 권준성 (울산대학교 의과대학 강릉아산병원 내과) ;
  • 김수희 (울산대학교 의과대학 강릉아산병원 내과) ;
  • 최건무 (울산대학교 의과대학 강릉아산병원 일반외과) ;
  • 엄대운 (울산대학교 의과대학 강릉아산병원 병리과) ;
  • 송경일 (울산대학교 의과대학 강릉아산병원 내과)
  • Received : 2013.04.07
  • Accepted : 2013.08.12
  • Published : 2013.12.01

Abstract

Encapsulating peritoneal fibrosis (EPF) is a serious, uncommon complication of chronic peritoneal dialysis. However, it is rare in hemodialysis patients. EPF is characterized by peritoneal membrane inflammation followed by peritoneal membrane fibrosis and encapsulation. The etiology is unclear, but inflammation of the deteriorated peritoneum causes peritoneal fibrosis. We present a case of EPF that occurred in a 29-year-old man with hepatitis B-associated liver cirrhosis with ascites that was treated solely with hemodialysis. We managed this patient surgically and then medically with prednisolone. To our knowledge, this is the first such case in Korea, so we report this case with a literature review.

저자들은 B형 간염에 의한 간경화가 있는 혈액투석 환자에서 반복적인 복수 및 복막염의 증상이 발생하여 경화성 복막염 의심하에 개복술로 이를 확진하였고 이후 스테로이드 치료로 호전된 경화성 피막성 복막염을 1예를 경험하였기에 문헌고찰과 함께 보고하는 바이다.

Keywords

References

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