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성인에서 폐동맥판협착과 난원공개존증을 동반한 동맥관개존증 1예

A Case of Asymptomatic Severe Pulmonary Valve Stenosis with Patent Foramen Ovale and Patent Ductus Arteriosus in an Adult

  • 김선아 (가톨릭대학교 의과대학 내과학교실 심장내과) ;
  • 허성호 (가톨릭대학교 의과대학 내과학교실 심장내과) ;
  • 박만원 (가톨릭대학교 의과대학 내과학교실 심장내과) ;
  • 나수진 (가톨릭대학교 의과대학 내과학교실 심장내과) ;
  • 김형덕 (가톨릭대학교 의과대학 내과학교실 심장내과) ;
  • 김지은 (가톨릭대학교 의과대학 내과학교실 심장내과) ;
  • 김우현 (가톨릭대학교 의과대학 내과학교실 심장내과)
  • Kim, Seon A (Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea College of Medicine) ;
  • Her, Sung-Ho (Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea College of Medicine) ;
  • Park, Mahn Won (Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea College of Medicine) ;
  • Na, Soo Jin (Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea College of Medicine) ;
  • Kim, Hyung Duk (Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea College of Medicine) ;
  • Kim, Ji Eun (Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea College of Medicine) ;
  • Kim, Woo Hyeon (Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea College of Medicine)
  • 투고 : 2012.08.31
  • 심사 : 2012.11.02
  • 발행 : 2013.10.01

초록

저자들은 중증 폐동맥판협착과 난원공개존증이 있음에도 동맥관개존증이 동반되어 무증상으로 나타난 성인에서의 증례를 경험하였기에 이를 문헌고찰과 함께 보고하는 바이다.

Pulmonary valve stenosis (PS) is the 3rd most common form of adult congenital heart disease. The patient was a 56-year-old woman, with known congenital heart disease but who was not receiving any treatment as she was not functionally limited. A two-dimensional echocardiogram showed severe right ventricular hypertrophy, pulmonary valve thickening and systolic doming. A color Doppler revealed a retrograde flow from the aorta to the left pulmonary artery. She had severe heart failure on the right hand side from a PS but did not display any symptoms. We hypothesized that she had a retrograde flow to the pulmonary circulation through a patent ductus arteriosus (PDA), through which oxygenated blood could be supplied to the systemic circulation and, hence, no hypoxia. We attempted a balloon valvuloplasty for the PS followed by a device closure for the PDA. Here we report on this adult female with severe PS but lacking any symptoms, due to the presence of a PDA.

키워드

참고문헌

  1. Rocchini AP, Emmanouilides GC. Moss and Adams heart disease in infants, children, and adolescents. 5th ed. Baltimore: Williams & Wilkins, 1995.
  2. Bonow RO, Carabello BA, Chatterjee K, et al. 2008 focused update incorporated into the ACC/AHA 2006 guidelines for the management of patients with valvular heart disease: a report of the American College of Cardiology/American Heart Association Task Force on Practice Guidelines (writing committee to revise the 1998 guidelines for the management of patients with valvular heart disease): endorsed by the Society of Cardiovascular Anesthesiologists, Society for Cardiovascular Angiography and Interventions, and Society of Thoracic Surgeons. Circulation 2008;118:e523-661. https://doi.org/10.1161/CIRCULATIONAHA.108.190748
  3. Giannoglou GD, Antoniadis AP, Chatzizisis YS, Louridas GE. Adult congenital heart disease investigated with cardiac catheterization over a 20-year period. Open Cardiovasc Med J 2009;3:124-127. https://doi.org/10.2174/1874192400903010124
  4. Odenwald T, Taylor AM. Pulmonary valve interventions. Expert Rev Cardiovasc Ther 2011;9:1445-1457. https://doi.org/10.1586/erc.11.150
  5. Warnes CA, Williams RG, Bashore TM, et al. ACC/AHA 2008 guidelines for the management of adults with congenital heart disease: executive summary: a report of the American College of Cardiology/American Heart Association Task Force on Practice Guidelines (writing committee to develop guidelines for the management of adults with congenital heart disease). Circulation 2008;118:2395-2451. https://doi.org/10.1161/CIRCULATIONAHA.108.190811
  6. Brickner ME, Hillis LD, Lange RA. Congenital heart disease in adults: first of two parts. N Engl J Med 2000; 342:256-263. https://doi.org/10.1056/NEJM200001273420407
  7. Santoro G, Bigazzi MC, Palladino MT, Carrozza M, Russo MG, Calabro R. One-step treatment of patent ductus arteriosus and pulmonary artery stenosis by cardiac catheterization. Catheter Cardiovasc Interv 2003;59:271-275. https://doi.org/10.1002/ccd.10507
  8. Gaio G, Santoro G, D'Alto M, et al. Transcatheter treatment of "pulmonary artery hypertension" due to patent ductus arteriosus and pulmonary artery stenosis. Tex Heart Inst J 2006;33:383-385.