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전신성 홍반성 낭창 환자에서 재발한 가역적 후두부 뇌병증 증후군의 비가역적 출혈성 합병증

Irreversible Hemorrhagic Complication of Recurrent Posterior Reversible Encephalopathy Syndrome in a Patient with Systemic Lupus Erythematosus

  • 김호균 (대구가톨릭대학교 의과대학 영상의학과) ;
  • 이희중 (경북대학교병원 영상의학과) ;
  • 신경민 (경북대학교 의학전문대학원 영상의학과)
  • Kim, Ho Kyun (Department of Radiology, Catholic University of Daegu School of Medicine) ;
  • Lee, Hui Joong (Department of Radiology, Kyungpook National University Hospital) ;
  • Shin, Kyung Min (Department of Radiology, Kyungpook National University, School of Medicine)
  • 투고 : 2012.11.01
  • 심사 : 2013.01.17
  • 발행 : 2013.06.30

초록

대부분의 가역적 후두부 뇌병증 증후군 (PRES)는 가역적인 경과를 보이나 출혈 또는 경색을 동반한 비가역적 경과들도 보고되고 있다. 전신성 홍반성 낭창 (SLE)과 관련된 PRES는 고혈압이나 면역억제제와 관련이 있다. 저자들은 최초 PRES발병 시 확산강조영상에서 확산제한을 보인 부위에서, PRESS의 반복 발생 시 출혈성 변환을 보인 증례를 보고한다.

Although most cases of posterior reversible encephalopathy syndrome (PRES) are reversible, irreversible lesions as a form of hemorrhage or infarction have been described. PRES as a complication of systemic lupus erythematosus (PRES-SLE) is associated with hypertension or use of immunosuppressive agents. We present a case of recurrent atypical PRES-SLE, which showed restricted diffusion in the first manifestation of SLE, resulted in parenchymal hemorrhagic transformations in the recurrent episode.

키워드

참고문헌

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