Korean Circulation Journal

The Korean Society of Cardiology (대한심장학회)
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Repeated Aborted Sudden Cardiac Death with Long QT Syndrome in a Patient with Anomalous Origin of the Right Coronary Artery from the Left Coronary Cusp

  • Park, Yae Min (Cardiology Division, Gachon University Gil Hospital) ;
  • Kim, Su Ji (Cardiology Division, Gachon University Gil Hospital) ;
  • Park, Chul-Hyun (Thoracic and Cardiovascular Surgery Division, Gachon University Gil Hospital) ;
  • Kang, Woong Chol (Cardiology Division, Gachon University Gil Hospital) ;
  • Shin, Mi-Seung (Cardiology Division, Gachon University Gil Hospital) ;
  • Koh, Kwang Kon (Cardiology Division, Gachon University Gil Hospital) ;
  • Choi, In Suck (Cardiology Division, Gachon University Gil Hospital)
  • Received : 2013.07.18
  • Accepted : 2013.08.22
  • Published : 2013.12.30
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Abstract

A 15-year-old female with a prior history of aborted cardiac death and surgical correction of anomalous origin of the right coronary artery (RCA) presented with polymorphic ventricular tachycardia. Her electrocardiogram after defibrillation was suggestive of congenital long QT syndrome (LQTS). The patient was treated with a ${\beta}$-blocker and remained free from ventricular arrhythmia during the follow-up of more than 6 months. Here, we present the case of a young female with repeated aborted cardiac death accompanied by anomalous origin of the RCA and congenital LQTS for the first time.

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References

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