Maxillofacial Plastic and Reconstructive Surgery

Korean Association of Maxillofacial Plastic and Reconstructive Surgeons (대한악안면성형재건외과학회)
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Osteonecrosis of Maxilla in Wegener's Granulomatosis: Case Report

상악골 괴사를 동반한 베게너 육아종증: 증례보고

  • Kim, Il-Kyu (Devision of Oral and Maxillofacial Surgery, Department of Dentistry, College of Medicine, Inha University) ;
  • Chang, Jae-Won (Devision of Oral and Maxillofacial Surgery, Department of Dentistry, College of Medicine, Inha University) ;
  • Ju, Sang-Hyun (Devision of Oral and Maxillofacial Surgery, Department of Dentistry, College of Medicine, Inha University) ;
  • Pyeon, Young-Hoon (Devision of Oral and Maxillofacial Surgery, Department of Dentistry, College of Medicine, Inha University) ;
  • Jung, Bum-Sang (Devision of Oral and Maxillofacial Surgery, Department of Dentistry, College of Medicine, Inha University) ;
  • Han, Ji-Young (Department of Pathology, College of Medicine, Inha University)
  • 김일규 (인하대학교 의과대학 치과학교실 구강악안면외과) ;
  • 장재원 (인하대학교 의과대학 치과학교실 구강악안면외과) ;
  • 주상현 (인하대학교 의과대학 치과학교실 구강악안면외과) ;
  • 편영훈 (인하대학교 의과대학 치과학교실 구강악안면외과) ;
  • 정범상 (인하대학교 의과대학 치과학교실 구강악안면외과) ;
  • 한지영 (인하대학교 의과대학 병리학교실)
  • Received : 2012.02.13
  • Accepted : 2012.05.04
  • Published : 2012.05.30
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Abstract

Wegener's granulomatosis (WG) is an autoimmune disease of unknown etiology characterized by the triad of necrotizing granulomatous lesion in the upper and lower respiratory tracts or both, disseminated vasculitis involving both small arteries and veins, and necrotizing glomerulonephritis. The most common oral lesions associated with WG are ulceration and strawberry gingivitis. A 47-years old man in medical care associated WG was consulted our Division of Oral and Maxillofacial Surgery for the chief complaint of toothaches. Pre-operative panorama showed the alveolar radiolucency and the loss of lamina dura regarding the left upper teeth. An oropharyngeal magnetic resonance imaging also revealed the increased bone marrow signal intensity on the left maxilla. Under the impression of maxillary osteonecrosis due to WG, maxillary saucerization with removal of involved teeth was performed. We obtained good results and report the first case of WG in Korea, with the review of literatures regarding oral and general systemic features.

Keywords

References

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