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TOTAL OCCLUSION OF RIGHT MAIN PULMONARY ARTERY IN A PATIENT WITH TAKAYASU'S ARTERITIS AND SEVERE PULMONARY HYPERTENSION

  • Choi, Hong-Mi (Department of Internal Medicine, Seoul National University College of Medicine, Cardiovascular Center, Seoul National University Hospital) ;
  • Kim, Hyung-Kwan (Department of Internal Medicine, Seoul National University College of Medicine, Cardiovascular Center, Seoul National University Hospital) ;
  • Shin, Hyo-Sun (Department of Internal Medicine, Seoul National University College of Medicine, Cardiovascular Center, Seoul National University Hospital) ;
  • Lee, Seung-Ah (Department of Internal Medicine, Seoul National University College of Medicine, Cardiovascular Center, Seoul National University Hospital) ;
  • Lee, Hee-Sun (Department of Internal Medicine, Seoul National University College of Medicine, Cardiovascular Center, Seoul National University Hospital) ;
  • Oh, Gyu-Chul (Department of Internal Medicine, Seoul National University College of Medicine, Cardiovascular Center, Seoul National University Hospital) ;
  • Lee, Seung-Pyo (Department of Internal Medicine, Seoul National University College of Medicine, Cardiovascular Center, Seoul National University Hospital) ;
  • Kim, Yong-Jin (Department of Internal Medicine, Seoul National University College of Medicine, Cardiovascular Center, Seoul National University Hospital) ;
  • Cho, Goo-Yeong (Department of Internal Medicine, Seoul National University College of Medicine, Cardiovascular Center, Seoul National University Bundang Hospital) ;
  • Sohn, Dae-Won (Department of Internal Medicine, Seoul National University College of Medicine, Cardiovascular Center, Seoul National University Hospital)
  • Received : 2012.06.21
  • Accepted : 2012.11.21
  • Published : 2012.12.27

Abstract

Takayasu's arteritis is a chronic inflammatory disorder that mainly involves medium to large sized arteries. Although pulmonary artery involvement is reported with a prevalence of about 10% to 50%, its clinical significance is underestimated. We report here one case of Takayasu's arteritis complicated by severe pulmonary hypertension due to right main pulmonary artery total occlusion.

Keywords

Cited by

  1. Prevalence of Coronary Artery-Pulmonary Artery Collaterals in Patients with Chronic Thromboembolic Pulmonary Hypertension vol.5, pp.2, 2012, https://doi.org/10.1086/681225