Annals of Clinical Neurophysiology

The Korean Society of Clinical Neurophysiology (대한임상신경생리학회)
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Nephrogenic Systemic Fibrosis with Myopathy

근병증을 동반한 콩팥성전신섬유화증

  • Heo, Deok-Hyun (Department of Neurology, Soonchunhyang University College of Medicine) ;
  • Jang, Il-Mi (Department of Neurology, Soonchunhyang University College of Medicine) ;
  • Roh, Hakjae (Department of Neurology, Soonchunhyang University College of Medicine) ;
  • Ahn, Moo-Young (Department of Neurology, Soonchunhyang University College of Medicine) ;
  • Jin, So-Young (Department of Pathology, Soonchunhyang University College of Medicine)
  • 허덕현 (순천향대학교 의과대학 신경과학교실) ;
  • 장일미 (순천향대학교 의과대학 신경과학교실) ;
  • 노학재 (순천향대학교 의과대학 신경과학교실) ;
  • 안무영 (순천향대학교 의과대학 신경과학교실) ;
  • 진소영 (순천향대학교 의과대학 병리학교실)
  • Received : 2011.11.01
  • Accepted : 2012.02.21
  • Published : 2012.06.30
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Abstract

Nephrogenic systemic fibrosis (NSF) is a systemic disease that affects the skin and other tissues in patients with renal insufficiency and exposure to gadolinium-containing contrast. A 55-year-old woman with end-stage renal disease on hemodialysis was consulted for progressive general weakness. After she had undergone multiple MRIs with gadolinium-containing contrast media, muscle weakness and skin lesions were developed. Her skin and muscle biopsy specimens showed CD34+ fibroblast entrapping collagen bundles. There are few reports of NSF with myopathy.

Keywords

References

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