Korean Circulation Journal

The Korean Society of Cardiology (대한심장학회)
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Two Cases of High Output Heart Failure Caused by Hereditary Hemorrhagic Telangiectasia

  • Cho, Donghyuk (Department of Cardiology, Korea University College of Medicine) ;
  • Kim, Sua (Department of Cardiology, Korea University College of Medicine) ;
  • Kim, Mina (Department of Cardiology, Korea University College of Medicine) ;
  • Seo, Young Ho (Department of Cardiology, Korea University College of Medicine) ;
  • Kim, Woohyeun (Department of Cardiology, Korea University College of Medicine) ;
  • Kang, Seong Hee (Department of Cardiology, Korea University College of Medicine) ;
  • Park, Sung-Mi (Department of Cardiology, Korea University College of Medicine) ;
  • Shim, Wanjoo (Department of Cardiology, Korea University College of Medicine)
  • Published : 2012.12.31
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Abstract

High-output cardiac failure is a rare complication of hereditary hemorrhagic telangiectasia (HHT) usually caused by shunting of blood through atriovenous malformations (AVMs) in the liver. We describe two cases of high output heart failure due to large hepatic AVMs. Clinical suspicion of HHT based on detailed history taking and physical examination is essential for early detection and proper management of heart failure associated with HHT.

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References

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  3. Cerebrovascular and cardiovascular disease burden in patients with hereditary hemorrhagic telangiectasia vol.42, pp.12, 2012, https://doi.org/10.1007/s10072-021-05135-z