Korean Circulation Journal

The Korean Society of Cardiology (대한심장학회)
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A Case of Left Ventricular Noncompaction Accompanying Fasciculo-Ventricular Accessory Pathway and Atrial Flutter

  • Yim, Sun Mie (Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea College of Medicine) ;
  • Jang, Sung-Won (Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea College of Medicine) ;
  • Chun, Hyun Ji (Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea College of Medicine) ;
  • Kim, Su Jung (Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea College of Medicine) ;
  • Choi, Kyu Young (Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea College of Medicine) ;
  • Kwon, Beom-June (Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea College of Medicine) ;
  • Kim, Dong-Bin (Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea College of Medicine) ;
  • Cho, Eun Joo (Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea College of Medicine) ;
  • Lee, Man-Young (Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea College of Medicine) ;
  • Rho, Tai-Ho (Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea College of Medicine) ;
  • Kim, Jae-Hyung (Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea College of Medicine)
  • Published : 2012.10.31
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Abstract

Left ventricular hypertrabeculation/noncompaction (LVHT) is an uncommon type of genetic cardiomyopathy characterized by trabeculations and recesses within the ventricular myocardium. LVHT is associated with diastolic or systolic dysfunction, thromboembolic complications, and arrhythmias, including atrial fibrillation, ventricular arrhythmias, atrioventricular block and Wolff-Parkinson-White syndrome. Herein, we describe a patient who presented with heart failure and widecomplex tachycardia. Echocardiography showed LVHT accompanied with severe mitral regurgitation. The electrophysiologic study revealed a fasciculo-ventricular accessory pathway and atrial flutter (AFL). The AFL was successfully treated with catheter ablation.

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References

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