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Deep Brain Stimulation of the Globus Pallidus in a 7-Year-Old Girl with DYT1 Generalized Dystonia

  • Jin, Seon Tak (Department of Neurosurgery, Maryknoll Medical Center) ;
  • Lee, Myung Ki (Department of Neurosurgery, Maryknoll Medical Center) ;
  • Ghang, Ju Young (Department of Neurosurgery, Bongseng Memorial Hospital) ;
  • Jeon, Seong Man (Department of Neurosurgery, Bongseng Memorial Hospital)
  • 투고 : 2012.03.23
  • 심사 : 2012.08.29
  • 발행 : 2012.09.28

초록

The experience of pediatric deep brain stimulation (DBS) of the globus pallidus internus (GPi) in the treatment of early-onset DYT1 generalized dystonia is still limited. Here, we report the surgical experience of bilateral GPi-DBS under general anesthesia by using microelectrode recording in a 7-year-old girl with early-onset DYT1 generalized dystonia. Excellent improvement of her dystonia without neurological complications was achieved. This case report demonstrates that GPi-DBS is an effective and safe method for the treatment of medically refractory early-onset DYT1 generalized dystonia in children.

키워드

참고문헌

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피인용 문헌

  1. Deep brain stimulation in children and young adults with secondary dystonia: the Children's Hospital Los Angeles experience vol.35, pp.5, 2012, https://doi.org/10.3171/2013.8.focus13300
  2. Deep brain stimulation in pediatric dystonia: a systematic review vol.43, pp.3, 2012, https://doi.org/10.1007/s10143-018-1047-9