DOI QR코드

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Epidemiology and Clinical Management of Pulmonary Hypertension in Children

  • Jin, Hongfang (Department of Pediatrics, Peking University First Hospital) ;
  • Yang, Jinyan (Department of Pediatrics, Peking University First Hospital) ;
  • Zhang, Qingyou (Department of Pediatrics, Peking University First Hospital) ;
  • Du, Junbao (Department of Pediatrics, Peking University First Hospital)
  • 발행 : 2012.08.31

초록

Pulmonary hypertension (PH) is a clinical hemodynamic syndrome characterized by increased pulmonary artery pressure and pulmonary vascular resistance. It can cause right ventricular failure, and even death. Pediatric PH is not very common, but is a greatly hazardous disease that leads to a high mortality rate. Therefore, many registry organizations have been established in the world to strengthen the study of diagnosis and treatment of the disease, and improve the understanding of pediatric PH. This article reviewed recently published researches, as well as presented a comprehensive understanding of PH, including definition, classification, epidemiology, prognosis and treatment.

키워드

참고문헌

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피인용 문헌

  1. Bosentan for Treatment of Pediatric Idiopathic Pulmonary Arterial Hypertension: State-of-the-Art vol.7, pp.None, 2012, https://doi.org/10.3389/fped.2019.00302