Korean Circulation Journal

  • 제42권2호
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  • Pages.136-139
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  • 2012
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  • 1738-5520(pISSN)
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  • 1738-5555(eISSN)
대한심장학회 (The Korean Society of Cardiology)
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A Case of Severe Aortic Valve Regurgitation Caused by an Ascending Aortic Aneurysm in a Young Patient With Autosomal Dominant Polycystic Kidney Disease and Normal Renal Function

  • Kim, Jeon-Geun (Regional Cardiovascular Center, Division of Cardiology, Department of Internal Medicine, Chungbuk National University School of Medicine) ;
  • Kim, Sang-Min (Regional Cardiovascular Center, Division of Cardiology, Department of Internal Medicine, Chungbuk National University School of Medicine) ;
  • Lee, Sang-Yeub (Regional Cardiovascular Center, Division of Cardiology, Department of Internal Medicine, Chungbuk National University School of Medicine) ;
  • Lee, Ho-Chang (Department of Pathology, Chungbuk National University School of Medicine) ;
  • Bae, Jang-Whan (Regional Cardiovascular Center, Division of Cardiology, Department of Internal Medicine, Chungbuk National University School of Medicine) ;
  • Hwang, Kyung-Kuk (Regional Cardiovascular Center, Division of Cardiology, Department of Internal Medicine, Chungbuk National University School of Medicine) ;
  • Kim, Dong-Woon (Regional Cardiovascular Center, Division of Cardiology, Department of Internal Medicine, Chungbuk National University School of Medicine) ;
  • Cho, Myeong-Chan (Regional Cardiovascular Center, Division of Cardiology, Department of Internal Medicine, Chungbuk National University School of Medicine) ;
  • Byeon, Sun-Ju (Department of Pathology, College of Medicine, Seoul National University) ;
  • Kim, Ki-Bong (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Seoul National University)
  • 발행 : 2012.02.29
⟨ 이전 논문 다음 논문 ⟩

초록

Aortic aneurysm is one several well-known cardiovascular complications in patients with autosomal dominant polycystic kidney disease (ADPCKD). Commonly affected site of aortic aneurysm and its related dissection in ADPCKD is abdominal aorta. Long standing hypertension, haemodialysis, old age are closely related with discovering of aortic aneurysm and dissection in ADPCKD. However, thoracic aortic aneurysms and its related severe aortic regurgitations (ARs) are rare in younger patients suffering from ADPCKD, especially ones who have normal renal function. Here, we report a case involving a 27-year-old Asian male patient with severe AR due to an ascending aneurysm of the thoracic aorta associated with ADPCKD. The patient had normal renal function without Marfan's habitus. The AR and thoracic aortic aneurysm were corrected surgically.

키워드

참고문헌

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피인용 문헌

  1. Dissecting Thoracoabdominal Aortic Aneurysm in a 15-Year-Old Boy With Polycystic Kidney Disease and Other Risk Factors vol.33, pp.7, 2012, https://doi.org/10.1007/s00246-012-0347-z
  2. Elastin and collagen fibre microstructure of the human aorta in ageing and disease: a review vol.10, pp.83, 2012, https://doi.org/10.1098/rsif.2012.1004
  3. A Pkd1-Fbn1 Genetic Interaction Implicates TGF-β Signaling in the Pathogenesis of Vascular Complications in Autosomal Dominant Polycystic Kidney Disease vol.25, pp.1, 2012, https://doi.org/10.1681/asn.2012050486
  4. Vascular complications in autosomal dominant polycystic kidney disease vol.11, pp.10, 2015, https://doi.org/10.1038/nrneph.2015.128