The Korean Journal of Medicine

  • 제83권1호
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  • Pages.150-155
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  • 2012
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  • 1738-9364(pISSN)
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  • 2289-0769(eISSN)
대한내과학회 (The Korean Association of Internal Medicine)
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피하낭종과 관절염의 형태로 나타난 Sweet 증후군 1예

A Case of Sweet's Syndrome Presenting as Subdermal Cystic Lesions and Arthritis

  • 기영재 (조선대학교 의과대학 내과학교실) ;
  • 조주연 (조선대학교 의과대학 내과학교실) ;
  • 정유진 (조선대학교 의과대학 내과학교실) ;
  • 김윤성 (조선대학교 의과대학 내과학교실) ;
  • 김현숙 (조선대학교 의과대학 내과학교실)
  • Ki, Young-Jae (Department of Internal Medicine, Chosun University College of Medicine) ;
  • Cho, Ju-Yeon (Department of Internal Medicine, Chosun University College of Medicine) ;
  • Jeong, Yu-Jin (Department of Internal Medicine, Chosun University College of Medicine) ;
  • Kim, Yun-Sung (Department of Internal Medicine, Chosun University College of Medicine) ;
  • Kim, Hyun-Sook (Department of Internal Medicine, Chosun University College of Medicine)
  • 발행 : 2012.07.01
⟨ 이전 논문 다음 논문 ⟩

초록

Sweet 증후군은 급성 열성 호중구성 피부질환으로 다양한 임상양상을 보일 수 있다. 피하 낭종을 포함하는 피부 병변, 관절염 및 구강내 궤양을 동반한 Sweet 증후군은 국내보고가 드물며 저자들은 초음파와 조직 생검을 통해 진단 후 스테로이드 전신 투여로 호전된 환자 1예를 경험하였기에 문헌고찰과 함께 보고하는 바이다.

Sweet's syndrome is characterized by a combination of clinical and pathologic findings including fever, neutrophilia, tender erythematous skin lesions, and a diffuse infiltration of mature neutrophils in the upper dermis. Numerous diseases and clinical manifestations have been associated with the disease; however, Sweet's syndrome associated with subdermal cystic skin lesions and arthritis is rare. A 71-year-old female patient presented with fever, erythematous plaques, multiple hypoglossal ulcers, and arthritis in both ankles. The skin lesions were variously sized areas of erythematous swelling on the forehead, back, and left shoulder. Musculoskeletal sonography revealed hypervascularity and a subdermal cyst in the erythematous plaque on her back. The results of a skin biopsy indicated the presence of mature neutrophilic infiltration in the dermis and thus led to the diagnosis of Sweet's syndrome. We herein present an unusual case of Sweet's syndrome presenting as erythematous subdermal cystic lesions, multiple hypoglossal ulcers, and bilateral ankle arthritis with a literature review.

키워드

참고문헌

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