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Renal Parenchymal Malakoplakia Presenting with Abscesses and Hepatic Extension Misdiagnosed as a Malignant Tumor: A Case Report

악성종양으로 오인된 화농성 병변과 간침범을 동반한 신 실질 연반증 1예

  • Yoon, Sun-Young (Department of Internal Medicine, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Lee, Hyo-Jeong (Department of Internal Medicine, Asan Medical Center, University of Ulsan College of Medicine) ;
  • An, Ji-Hyun (Department of Internal Medicine, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Kim, Su-Jeong (Department of Internal Medicine, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Kim, Sang-We (Department of Oncology, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Woo, Jun-Hee (Department of Infectious Diseases, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Kim, Yang-Soo (Department of Infectious Diseases, Asan Medical Center, University of Ulsan College of Medicine)
  • 윤선영 (울산대학교 의과대학 서울아산병원 내과) ;
  • 이효정 (울산대학교 의과대학 서울아산병원 내과) ;
  • 안지현 (울산대학교 의과대학 서울아산병원 내과) ;
  • 김수정 (울산대학교 의과대학 서울아산병원 내과) ;
  • 김상위 (울산대학교 의과대학 서울아산병원 종양내과) ;
  • 우준희 (울산대학교 의과대학 서울아산병원 감염내과) ;
  • 김양수 (울산대학교 의과대학 서울아산병원 감염내과)
  • Published : 2012.06.01

Abstract

Malakoplakia is a chronic inflammatory disorder that usually affects the urinary tract in immunocompromised patients and rarely extends to adjacent organs. Due to its mass-like presentation, malakoplakia is often clinically misdiagnosed as a neoplastic lesion. We describe the case of a 51-year-old female with renal malakoplakia and hepatic extension and large intraperitoneal abscesses that had been misdiagnosed as malignancy. She was diagnosed with myasthenia gravis 12 years prior and had been treated with oral corticosteroids and immunosuppressants. Radical nephrectomy concomitant with abscess drainage was performed. The final pathology was compatible with malakoplakia, and the patient was successfully treated with antibiotics. Although renal malakoplakia is a rare disease, it should be included in the differential diagnosis of patients with a renal mass who have a history of recurrent urinary tract infections or evidence of immunosuppression.

저자들은 악성종양으로 오인되었던 화농성 병변과 간 침범을 동반한 신실질의 연반증을 1예 경험하였고, 이에 대한 국내 보고가 없어 국내에서 보고된 연반증 증례 고찰과 함께 보고하는 바이다.

Keywords

References

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Cited by

  1. Renal Parenchymal Malakoplakia with Acute Interstitial Nephritis Presented with Acute Kidney Injury vol.38, pp.1, 2012, https://doi.org/10.12771/emj.2015.38.1.36
  2. Renal Malakoplakia with Wide Extension into the Retroperitoneum: A Case Report vol.73, pp.1, 2012, https://doi.org/10.3348/jksr.2015.73.1.62